{"id":"W2946497386","doi":"10.3899/jrheum.180820","title":"Thirty Years of Followup in 3 Patients with Familial Polyarteritis Nodosa due to Adenosine Deaminase 2 Deficiency","year":2019,"lang":"en","type":"letter","venue":"The Journal of Rheumatology","topic":"Vasculitis and related conditions","field":"Medicine","cited_by":8,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"National Institutes of Health; Margaret A. Cargill Foundation; Johns Hopkins University","keywords":"Medicine; Polyarteritis nodosa; Abdominal pain; Surgery; Internal medicine; Prednisone; Hematochezia; Vasculitis; Colonoscopy; Cancer","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005233315,0.0007589596,0.000582597,0.001109376,0.0023426,0.0007495504,0.0003951112,0.001116062,0.00101981],"category_scores_gemma":[0.002386618,0.0006660993,0.0008696608,0.0006915118,0.0005909506,0.0005352686,0.0008253271,0.0009464262,0.0002515098],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006998182,"about_ca_system_score_gemma":0.0004706404,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005087603,"about_ca_topic_score_gemma":0.00614494,"domain_scores_codex":[0.9994791,0.00008648424,0.0000658905,0.0001223411,0.00007687953,0.0001693347],"domain_scores_gemma":[0.9987773,0.0002585891,0.0003525412,0.00009526309,0.0001097243,0.0004065157],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0004236008,0.0002476261,0.8535106,0.00002169072,0.00006328853,0.1351316,0.003735559,0.00009376008,0.002076417,0.00007556161,0.0001970764,0.004423236],"study_design_scores_gemma":[0.00006922154,0.0009133568,0.8477499,0.00002388749,0.00008732417,0.1478877,0.001505286,0.0002362954,0.000370397,0.0001511603,0.0009679921,0.00003744807],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9992154,0.0002050426,0.00005972233,0.00005279276,0.00001365673,0.000008158261,0.00003232547,0.000004785441,0.0004080888],"genre_scores_gemma":[0.9993944,0.00009819109,0.00007238927,0.00007733546,0.0000238512,0.000009064834,0.00009937327,0.000003481083,0.000221881],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005087603,"threshold_uncertainty_score":0.01011598,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005203027096209734,"score_gpt":0.2101434815368523,"score_spread":0.2049404544406426,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}