{"id":"W2947844651","doi":"","title":"Cyclopentanoid D-Galactosidase Inhibitors and potential Pharmacological Chaperones for GM1-Gangliosidosis","year":2018,"lang":"en","type":"article","venue":"","topic":"Glycosylation and Glycoproteins Research","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of British Columbia","funders":"","keywords":"Gangliosidosis; Chemistry; Biochemistry; Enzyme","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001382541,0.000229886,0.0002767172,0.0002191341,0.0001613189,0.0002403356,0.0002312565,0.0002086538,0.001031608],"category_scores_gemma":[0.0000726751,0.0001051948,0.0001791924,0.0001920853,0.0001873841,0.000220809,0.0001326403,0.0005562797,0.0001869312],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000294753,"about_ca_system_score_gemma":0.0003093395,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007234084,"about_ca_topic_score_gemma":0.00169124,"domain_scores_codex":[0.9999702,0.000005172232,0.000002904449,0.000003214929,0.000004762085,0.00001373341],"domain_scores_gemma":[0.9999744,0.000004445921,0.000006877196,0.000002214622,0.000003723385,0.000008407879],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.005762314,0.0006028919,0.0006608691,0.0005859343,0.00008312678,0.0006396496,0.00006401329,0.0009944434,0.9067548,0.003135116,0.002106997,0.07860991],"study_design_scores_gemma":[0.001581151,0.004675845,0.008015696,0.00009419199,0.0002934683,0.001446254,0.0001015017,0.001742524,0.9244428,0.001012732,0.05654956,0.00004421595],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9276574,0.06352416,0.001957843,0.001118662,0.0002128682,0.0001027557,0.0005133064,0.000187848,0.004725212],"genre_scores_gemma":[0.9533209,0.04117279,0.001663695,0.0002367694,0.00008280675,0.00006811439,0.0005954824,0.00001625942,0.00284319],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001031608,"threshold_uncertainty_score":0.003451049,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01313603883302971,"score_gpt":0.2986254790298264,"score_spread":0.2854894401967967,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}