{"id":"W2948469016","doi":"10.1002/ana.25520","title":"Presymptomatic spinal cord pathology in <i>c9orf72</i> mutation carriers: A longitudinal neuroimaging study","year":2019,"lang":"en","type":"article","venue":"Annals of Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":91,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Polytechnique Montréal; Montreal Neurological Institute and Hospital","funders":"Agence Nationale de la Recherche","keywords":"C9orf72; Fractional anisotropy; Asymptomatic; Amyotrophic lateral sclerosis; Atrophy; Medicine; Diffusion MRI; White matter; Corticospinal tract; Magnetic resonance imaging; Neuroimaging; Spinal cord; Frontotemporal dementia; Pathology; Internal medicine; Dementia; Radiology; Disease; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004631427,0.0003968865,0.0002976294,0.0006769819,0.0009053978,0.0004802219,0.000248907,0.0005985333,0.0009719136],"category_scores_gemma":[0.001086639,0.0002426471,0.0002652392,0.0004342592,0.0003071258,0.0004413907,0.0002975908,0.0004009358,0.0003801209],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003126128,"about_ca_system_score_gemma":0.0003403179,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01018503,"about_ca_topic_score_gemma":0.00903197,"domain_scores_codex":[0.9998249,0.00002314282,0.00001787329,0.00006926111,0.00002622398,0.00003862731],"domain_scores_gemma":[0.9993,0.00006183928,0.0002513253,0.00004183545,0.0001673541,0.000177564],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0008861578,0.0002368296,0.9870004,0.00001379133,0.00007594517,0.001069424,0.0004365182,0.00004582284,0.00700932,0.00001580615,0.0001258092,0.00308418],"study_design_scores_gemma":[0.000009881524,0.0004484334,0.9979207,0.000005045872,0.00003241282,0.001022962,0.0001084988,0.00009658738,0.000220912,0.0000111799,0.0001186073,0.000004798449],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9996947,0.00006872857,0.00003063957,0.000007847803,0.000001428724,0.000006013528,0.00008507315,0.000002451608,0.0001031233],"genre_scores_gemma":[0.9993615,0.0000750852,0.0001002515,0.00001182456,0.000005500157,0.000009011543,0.0002816857,0.00000221986,0.0001529988],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01018503,"threshold_uncertainty_score":0.02025151,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.09364216495573333,"score_gpt":0.3965108161733332,"score_spread":0.3028686512175999,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}