{"id":"W2949086036","doi":"10.1136/annrheumdis-2019-eular.3341","title":"OP0204 EMAPALUMAB, AN INTERFERON GAMMA (IFN-Y)-BLOCKING MONOCLONAL ANTIBODY, IN PATIENTS WITH MACROPHAGE ACTIVATION SYNDROME (MAS) COMPLICATING SYSTEMIC JUVENILE IDIOPATHIC ARTHRITIS (SJIA)","year":2019,"lang":"en","type":"article","venue":"Annals of the Rheumatic Diseases","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":34,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Medicine; Macrophage activation syndrome; Hemophagocytosis; Arthritis; Internal medicine; Immunology; Hepatosplenomegaly; Gastroenterology; Tocilizumab; Adverse effect; Rheumatoid arthritis; Pancytopenia; Bone marrow; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004195587,0.0002455524,0.0008034382,0.0002022105,0.0001139769,0.00004708229,0.0003883156,0.00007983466,0.0001233871],"category_scores_gemma":[0.0002075814,0.0001792316,0.0001520305,0.0003599554,0.0001170318,0.0004154407,0.0001658119,0.0002667513,0.00004436825],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00006536352,"about_ca_system_score_gemma":0.0002113967,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001666038,"about_ca_topic_score_gemma":0.0000074337,"domain_scores_codex":[0.9973924,0.0002451703,0.000867871,0.0003516566,0.0007373356,0.0004055467],"domain_scores_gemma":[0.9981799,0.00008785261,0.0005306847,0.0008125899,0.0002534726,0.0001355142],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001277853,0.001459686,0.9432178,0.003898794,0.0002372192,0.00001848355,0.001147653,0.0005494534,0.002004723,0.000124759,0.00008603083,0.04597753],"study_design_scores_gemma":[0.003031302,0.001173014,0.9730598,0.01806406,0.00003432295,0.00003455913,0.0007492779,0.002565633,0.0009123893,0.0001367633,0.000008727075,0.0002302005],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9968249,0.001273621,0.00004012815,0.0002330088,0.00005842153,0.001353713,0.00002981373,0.0000440707,0.0001423614],"genre_scores_gemma":[0.999481,0.00010374,0.00002828086,0.0001005228,0.000009754674,0.00005612786,0.00009831037,0.00004495274,0.00007727383],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.04574733,"threshold_uncertainty_score":0.7308852,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02041723704868489,"score_gpt":0.2922752010956766,"score_spread":0.2718579640469917,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}