{"id":"W2952744832","doi":"10.1093/ndt/gfz106.fp114","title":"FP114RENOPROTECTIVE EFFECT OF AGALSIDASE ALFA IN FABRY DISEASE IS INDEPENDENT OF TYPE OF MUTATION: RESULTS OF 12-YEAR FOLLOW-UP","year":2019,"lang":"en","type":"article","venue":"Nephrology Dialysis Transplantation","topic":"Child Nutrition and Feeding Issues","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Dalhousie University","funders":"","keywords":"Medicine; Fabry disease; Internal medicine; Pediatrics; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001504346,0.0002724337,0.0004505517,0.0007577539,0.0002680219,0.0005410801,0.0002807517,0.0003295524,0.0008178907],"category_scores_gemma":[0.002124824,0.0001063633,0.0007622968,0.0006402858,0.0001804974,0.0003954956,0.0003479855,0.0003975792,0.0002149691],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003534499,"about_ca_system_score_gemma":0.0002006671,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002716636,"about_ca_topic_score_gemma":0.001828706,"domain_scores_codex":[0.9994919,0.0001232213,0.00005740605,0.0001115529,0.0001067171,0.0001090407],"domain_scores_gemma":[0.9980837,0.0003205805,0.0009838751,0.0001519645,0.0002399078,0.0002200224],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0009193916,0.00008413129,0.994082,0.000009002179,0.0001175976,0.0001184576,0.00005249305,0.00009073516,0.00028186,0.000005939521,0.00005717445,0.004181271],"study_design_scores_gemma":[0.00000980807,0.0003003103,0.9991239,0.000002869927,0.00007051098,0.0001437324,0.00002880606,0.0001004142,0.000126224,0.000006436051,0.00008420175,0.000002808262],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9991346,0.0002641477,0.00006047995,0.00001317783,0.00000243026,0.000003897124,0.0003179388,0.000003007196,0.000200427],"genre_scores_gemma":[0.9993048,0.0000662855,0.00003484756,0.000006808711,0.000004904055,0.000002866808,0.0004560873,9.75692e-7,0.0001224187],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002716636,"threshold_uncertainty_score":0,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01185345386432261,"score_gpt":0.2695057071562229,"score_spread":0.2576522532919002,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}