{"id":"W2973201228","doi":"10.1055/s-0039-1696657","title":"The International Prospective Glanzmann Thrombasthenia Registry: Pediatric Treatment and Outcomes","year":2019,"lang":"en","type":"article","venue":"TH Open","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":15,"is_retracted":false,"has_abstract":true,"ca_institutions":"Foothills Medical Centre; University of Calgary","funders":"Novo Nordisk","keywords":"Glanzmann's thrombasthenia; Thrombasthenia; Medicine; Pediatrics; Prospective cohort study; Patient registry; Internal medicine; Platelet; Platelet aggregation","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001439431,0.0003489137,0.0005771701,0.002233064,0.000258107,0.000650868,0.0005515395,0.0003489705,0.002850673],"category_scores_gemma":[0.004190573,0.0002449894,0.000389524,0.005620173,0.0002279631,0.0009122607,0.0006340324,0.0007218355,0.0007611851],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006596168,"about_ca_system_score_gemma":0.001622742,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005230153,"about_ca_topic_score_gemma":0.004437859,"domain_scores_codex":[0.9981311,0.0004464329,0.0003523084,0.0004259335,0.000415564,0.0002286329],"domain_scores_gemma":[0.9913687,0.0008034065,0.005566361,0.0005271647,0.00103356,0.0007006728],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003719865,0.00007338881,0.9783083,0.0001330482,0.000175048,0.00009044584,0.00005428663,0.00033536,0.00008438595,0.0003174858,0.01338533,0.006671052],"study_design_scores_gemma":[0.000198233,0.0001608809,0.9917592,0.0001198356,0.0001451583,0.0006649614,0.0001242289,0.000481914,0.0001963423,0.0001115494,0.006023526,0.00001409237],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.7586145,0.004533472,0.001647156,0.0007878421,0.00009319909,0.0004251802,0.2215655,0.0001880813,0.01214513],"genre_scores_gemma":[0.7651569,0.004121162,0.002249035,0.0002902168,0.0001562892,0.001094529,0.2256928,0.00008496615,0.001154215],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005230153,"threshold_uncertainty_score":0.01039946,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01468954790454958,"score_gpt":0.3025458601901239,"score_spread":0.2878563122855743,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}