{"id":"W2973201228","doi":"10.1055/s-0039-1696657","title":"The International Prospective Glanzmann Thrombasthenia Registry: Pediatric Treatment and Outcomes","year":2019,"lang":"en","type":"article","venue":"TH Open","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":15,"is_retracted":false,"has_abstract":true,"ca_institutions":"Foothills Medical Centre; University of Calgary","funders":"Novo Nordisk","keywords":"Glanzmann's thrombasthenia; Thrombasthenia; Medicine; Pediatrics; Prospective cohort study; Patient registry; Internal medicine; Platelet; Platelet aggregation","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00005932061,0.0000955156,0.0001868233,0.0000176943,0.00007637028,0.00008600154,0.0001441706,0.0000238479,0.0001041708],"category_scores_gemma":[0.00001366499,0.00004819991,0.00003089343,0.00003922983,0.00002086542,0.00007281366,0.0001000317,0.00004050592,0.0001665941],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00007694002,"about_ca_system_score_gemma":0.00005246388,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002683748,"about_ca_topic_score_gemma":0.00007838139,"domain_scores_codex":[0.9995192,0.000008627918,0.00008635272,0.0001716052,0.0001006806,0.0001135039],"domain_scores_gemma":[0.999627,0.00004637353,0.00004829956,0.0002118845,0.00002389146,0.00004257281],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001737799,0.0001492265,0.9945331,0.00000335188,0.0002184576,0.00003230723,0.0002046627,1.803133e-7,0.00001267691,0.0007729363,0.00102563,0.002873727],"study_design_scores_gemma":[0.004988715,0.0004355994,0.9762755,0.000007831247,0.0001004889,0.00005430685,0.0001910691,0.00002090474,0.0000607036,0.00107225,0.01671922,0.00007338975],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9474925,0.0002416729,5.688096e-7,0.003231079,0.0001300716,0.0009375977,0.00001352425,0.00001427909,0.04793864],"genre_scores_gemma":[0.9697138,0.0004202835,0.0000852954,0.0001707156,0.00003738849,0.00005084368,0.00002341819,0.000009384567,0.02948885],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02222125,"threshold_uncertainty_score":0.2141285,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01468954790454958,"score_gpt":0.3025458601901239,"score_spread":0.2878563122855743,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}