{"id":"W2979572603","doi":"10.1016/j.cjca.2019.09.021","title":"Reversible Mitochondrial Fragmentation in iPSC-Derived Cardiomyocytes From Children With DCMA, a Mitochondrial Cardiomyopathy","year":2019,"lang":"en","type":"article","venue":"Canadian Journal of Cardiology","topic":"Mitochondrial Function and Pathology","field":"Biochemistry, Genetics and Molecular Biology","cited_by":40,"is_retracted":false,"has_abstract":false,"ca_institutions":"Libin Cardiovascular Institute of Alberta; Hotchkiss Brain Institute; St. Boniface Hospital; Alberta Children's Hospital; University of Manitoba; University of Calgary","funders":"Alberta Children's Hospital Foundation; Children's Cardiomyopathy Foundation","keywords":"Medicine; Cardiomyopathy; Fragmentation (computing); Mitochondrial DNA; Cardiology; Internal medicine; Genetics; Heart failure","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000381096,0.000228186,0.0003633806,0.0003035899,0.0003083007,0.0003587021,0.0003064072,0.0006305123,0.0024685],"category_scores_gemma":[0.0005588894,0.0001589262,0.000370006,0.0002173271,0.0005571831,0.0003627405,0.0004426664,0.001300795,0.0004966692],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002896882,"about_ca_system_score_gemma":0.0002628105,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005427969,"about_ca_topic_score_gemma":0.0006501826,"domain_scores_codex":[0.9996672,0.00003092055,0.00004957808,0.00008875244,0.0001034986,0.00006009656],"domain_scores_gemma":[0.9996338,0.00009513941,0.00007915388,0.00007063784,0.0000469953,0.00007437322],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.001217727,0.000213243,0.008069021,0.0002492311,0.00007136862,0.01317492,0.0005140577,0.0004714869,0.9623898,0.0008400406,0.0008075383,0.01198153],"study_design_scores_gemma":[0.0004849101,0.003445175,0.1611793,0.0001757169,0.0002450194,0.07542212,0.001417836,0.00251242,0.7418253,0.001226396,0.01199891,0.00006691645],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9926021,0.001172791,0.002298023,0.0002350482,0.0001331811,0.00006181323,0.001138891,0.00006830236,0.002289857],"genre_scores_gemma":[0.996958,0.000456424,0.0007211199,0.0001225067,0.00001861215,0.00004487166,0.0008756532,0.0000218952,0.0007808312],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0024685,"threshold_uncertainty_score":0.008257926,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.006607523210607356,"score_gpt":0.2020057787482283,"score_spread":0.195398255537621,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}