{"id":"W2983139950","doi":"10.1182/blood-2019-123817","title":"Sporadic Late Onset Nemaline Myopathy with a Monoclonal Gammopathy: Comparative Effectiveness of Immuno- and Chemotherapy","year":2019,"lang":"en","type":"article","venue":"Blood","topic":"Biochemical and Molecular Research","field":"Biochemistry, Genetics and Molecular Biology","cited_by":3,"is_retracted":false,"has_abstract":true,"ca_institutions":"Royal Victoria Regional Health Centre; Western University","funders":"","keywords":"Nemaline myopathy; Medicine; Monoclonal gammopathy of undetermined significance; Internal medicine; Plasmapheresis; Chemotherapy; Rituximab; Autologous stem-cell transplantation; Gammopathy; Gastroenterology; Oncology; Monoclonal; Myopathy; Lymphoma; Immunology; Monoclonal antibody; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001844075,0.0001404602,0.0002338742,0.00002859589,0.00002207826,0.00001006658,0.0001152064,0.00009495099,0.00001303217],"category_scores_gemma":[0.000008133341,0.0001093488,0.00005034817,0.00008471852,0.0001360925,0.000002636437,0.000068814,0.00009381387,0.000004793272],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000003131365,"about_ca_system_score_gemma":0.00006069806,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000022591,"about_ca_topic_score_gemma":0.000001912722,"domain_scores_codex":[0.9991882,0.00008629431,0.0001174695,0.0002975329,0.0001303007,0.0001802138],"domain_scores_gemma":[0.9995303,0.00002069659,0.00005535689,0.0002445733,0.00008209768,0.00006696712],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.001112263,0.0002629719,0.05218082,0.0001006014,0.0001454127,0.000006339339,0.00003717046,0.000004484142,0.9459682,0.00002360149,0.00001079118,0.0001473505],"study_design_scores_gemma":[0.003443359,0.001116616,0.06039151,0.00006023462,0.00002429322,0.00003835772,0.00002514456,0.00001926881,0.9343089,0.00003662852,0.0003855781,0.0001500487],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9978209,0.001346745,0.00009784847,0.00002785928,0.00001240129,0.0003334805,0.00002422817,0.000005798196,0.000330759],"genre_scores_gemma":[0.9991716,0.000118836,0.0003642527,0.00005751268,0.00002159744,0.00001812792,0.0001092573,0.00001665808,0.0001222288],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01165924,"threshold_uncertainty_score":0.4459116,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.006077282773513147,"score_gpt":0.2438882026530692,"score_spread":0.237810919879556,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}