{"id":"W2991473615","doi":"10.6000/2292-2598.2019.07.04.7","title":"Does Late-Onset Huntington Disease Represent a Distinct Symptomatic Picture? Evidence for a Selective Deficit in Executive Function and Emotion Recognition, in the Absence of Behavioral and Psychiatric Disorders","year":2019,"lang":"en","type":"article","venue":"Journal of Intellectual Disability - Diagnosis and Treatment","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Huntington's disease; Psychology; Executive functions; Psychiatry; Disease; Executive dysfunction; Cognition; Clinical psychology; Medicine; Neuropsychology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002367095,0.0005294587,0.0006094521,0.0008053244,0.0003337939,0.0005723813,0.0003043401,0.001254256,0.001732881],"category_scores_gemma":[0.0007583195,0.000205325,0.0002210559,0.0003046522,0.00060651,0.0007371518,0.0004492766,0.0004574145,0.0003368714],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001662771,"about_ca_system_score_gemma":0.0002197337,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0006660488,"about_ca_topic_score_gemma":0.0008480513,"domain_scores_codex":[0.9999167,0.00001140173,0.00001377808,0.00002221069,0.00001201105,0.00002387208],"domain_scores_gemma":[0.9996928,0.00007769837,0.00009078057,0.00002389639,0.00003086165,0.00008395422],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001990431,0.0003436474,0.6472864,0.0002677046,0.00008027983,0.2876299,0.001682931,0.0001350599,0.03476866,0.001218719,0.0007350838,0.02386121],"study_design_scores_gemma":[0.0000713616,0.0008059533,0.5462111,0.00007595107,0.00007152663,0.4461167,0.001003893,0.0004764644,0.001890644,0.001428867,0.00181698,0.00003050548],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.995415,0.001405098,0.0002928568,0.0003710196,0.00001921042,0.00001748707,0.0001172484,0.00001225222,0.002349887],"genre_scores_gemma":[0.9984893,0.0004526743,0.0001679769,0.0002038663,0.00007966557,0.000005986382,0.0001964602,0.000004071798,0.000400099],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001732881,"threshold_uncertainty_score":0.005797088,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04653973840841107,"score_gpt":0.3112568425045466,"score_spread":0.2647171040961355,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}