{"id":"W2991518933","doi":"10.3389/fped.2019.00481","title":"Hematopoietic Stem Cell Transplantation for Severe Combined Immunodeficiency (SCID)","year":2019,"lang":"en","type":"review","venue":"Frontiers in Pediatrics","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":41,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier Universitaire Sainte-Justine; Université de Montréal","funders":"","keywords":"Severe combined immunodeficiency; Medicine; Hematopoietic stem cell transplantation; Transplantation; Stem cell; Immunodeficiency; Hematopoietic cell; Primary immunodeficiency; Immunology; Haematopoiesis; Internal medicine; Immune system; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0005837015,0.0007362981,0.002253601,0.0008247628,0.0002544173,0.00004370954,0.0009930548,0.001293046,0.00004630633],"category_scores_gemma":[0.00002170904,0.0006879457,0.0008530133,0.0009027715,0.0001412788,0.0001565009,0.00007573987,0.0009379893,0.0003457623],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002026241,"about_ca_system_score_gemma":0.0005698387,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001419264,"about_ca_topic_score_gemma":4.085263e-7,"domain_scores_codex":[0.9965516,0.0003122395,0.001329033,0.0008005747,0.00008929651,0.0009172664],"domain_scores_gemma":[0.9981484,0.0003637395,0.0007100472,0.0006920192,0.00007480672,0.00001101223],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001727397,0.0005087307,0.00007787297,0.05486404,0.0001287758,0.000007038044,0.001475931,0.00003976145,0.000007395264,0.0002185248,0.006726883,0.9357723],"study_design_scores_gemma":[0.002672249,0.0002357523,0.00001178796,0.001296984,0.00176823,0.00005211656,0.0008268958,0.000008149946,0.00001111102,0.0001410945,0.9919226,0.001053073],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00008734678,0.9828125,0.003948575,0.000008086634,0.00927632,0.0024154,0.0004331402,0.00009662267,0.0009219965],"genre_scores_gemma":[0.0005617521,0.9916676,0.0001711043,0.00002553502,0.00001343774,0.0002947993,0.002058254,0.0001093953,0.005098114],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.9851957,"threshold_uncertainty_score":0.9995572,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01620522507733124,"score_gpt":0.2498535441674815,"score_spread":0.2336483190901503,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}