{"id":"W2997341269","doi":"10.1097/eja.0000000000001061","title":"Atypical clinical presentation of variant Creutzfeldt–Jakob disease","year":2019,"lang":"en","type":"letter","venue":"European Journal of Anaesthesiology","topic":"Prion Diseases and Protein Misfolding","field":"Biochemistry, Genetics and Molecular Biology","cited_by":20,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Bovine spongiform encephalopathy; Medicine; Disease; Transmission (telecommunications); Outbreak; Creutzfeldt-Jakob Syndrome; Pathology; Fatal familial insomnia; Transmissible spongiform encephalopathy; Prion protein; Virology; Scrapie","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006294355,0.002217637,0.002176606,0.002234675,0.001067949,0.001682959,0.002085797,0.00546613,0.005587672],"category_scores_gemma":[0.004231061,0.0007426537,0.0009391279,0.0009994602,0.001090753,0.002508343,0.000805722,0.003603283,0.002367474],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000920428,"about_ca_system_score_gemma":0.000497232,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001463426,"about_ca_topic_score_gemma":0.001628719,"domain_scores_codex":[0.9990675,0.0001501796,0.0001349072,0.0002643426,0.0001454065,0.000237659],"domain_scores_gemma":[0.9984054,0.0005908696,0.0001998936,0.00007114813,0.0003296238,0.0004029273],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001968069,0.0001046098,0.007912626,0.0002356613,0.00005216967,0.9576677,0.0001278098,0.0001878677,0.001317554,0.0004395761,0.02500809,0.006749394],"study_design_scores_gemma":[0.00005822123,0.0000864172,0.006384718,0.0001733634,0.00003883733,0.9826817,0.00006763842,0.0009477653,0.000322775,0.0004360982,0.008767056,0.00003538719],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.5610992,0.07210082,0.01561298,0.1254655,0.08021425,0.001297566,0.002603275,0.001386083,0.1402204],"genre_scores_gemma":[0.8864073,0.01179747,0.003236672,0.02250891,0.06609323,0.0001375059,0.0005811152,0.0001359827,0.009101903],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005587672,"threshold_uncertainty_score":0.01869261,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02847698731641099,"score_gpt":0.2959185781392614,"score_spread":0.2674415908228505,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}