{"id":"W2997806446","doi":"10.1016/s2352-3026(19)30206-6","title":"Clinical features and outcomes of patients with Shwachman-Diamond syndrome and myelodysplastic syndrome or acute myeloid leukaemia: a multicentre, retrospective, cohort study","year":2019,"lang":"en","type":"article","venue":"The Lancet Haematology","topic":"Blood disorders and treatments","field":"Biochemistry, Genetics and Molecular Biology","cited_by":116,"is_retracted":false,"has_abstract":false,"ca_institutions":"Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"National Center for Advancing Translational Sciences; National Center for Research Resources; National Heart, Lung, and Blood Institute; National Institute of Diabetes and Digestive and Kidney Diseases; National Cancer Institute; National Institutes of Health","keywords":"Medicine; Myelodysplastic syndromes; Retrospective cohort study; Myeloid leukaemia; Cohort; Myeloid leukemia; Myeloid; Cohort study; Internal medicine; Pediatrics; Bone marrow","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006847754,0.0006612848,0.0009786582,0.0009191433,0.0007879463,0.001275174,0.0008066722,0.00120242,0.002036504],"category_scores_gemma":[0.002082594,0.0008053723,0.001097594,0.001708194,0.0007395071,0.00142248,0.001065927,0.001115756,0.0004786815],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006638896,"about_ca_system_score_gemma":0.0004254983,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005295971,"about_ca_topic_score_gemma":0.003047127,"domain_scores_codex":[0.9991666,0.0001733765,0.00008349837,0.0003068505,0.000103365,0.0001662988],"domain_scores_gemma":[0.998577,0.0001836098,0.0005444772,0.0001732691,0.0001238499,0.0003978359],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0006511949,0.00007302301,0.9975925,0.000009923965,0.0001570198,0.0003600456,0.0001082364,0.00004607283,0.0003906061,0.00002693154,0.00009736126,0.0004869545],"study_design_scores_gemma":[0.00004769117,0.0002818739,0.9978276,0.000006454084,0.00006874574,0.001102776,0.0003512872,0.0001094124,0.00003580034,0.00004072766,0.0001144856,0.00001315629],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9991432,0.0002204862,0.00003935067,0.00002194483,0.000006491569,0.000008929705,0.0003662931,0.000001982642,0.0001912149],"genre_scores_gemma":[0.9990734,0.0001176397,0.00004077805,0.00002644026,0.00001383294,0.00001185973,0.0005917371,0.000002528382,0.0001216825],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005295971,"threshold_uncertainty_score":0.01053029,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.007303935844791967,"score_gpt":0.2659708146748395,"score_spread":0.2586668788300476,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}