{"id":"W3007350570","doi":"10.1016/j.jaci.2019.12.537","title":"Immune thrombocytopenia (ITP) in the setting of hereditary angioedema with C1 inhibitor deficiency (HAE C1INH): a possible consequence of low C4","year":2020,"lang":"en","type":"article","venue":"Journal of Allergy and Clinical Immunology","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"McMaster University","funders":"","keywords":"Medicine; Hereditary angioedema; Prednisone; C1-inhibitor; Immune thrombocytopenia; Angioedema; Danazol; Pediatrics; Autoimmune lymphoproliferative syndrome; Platelet; Gastroenterology; Internal medicine; Immunology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004002507,0.0009331821,0.0006944583,0.001566692,0.001004653,0.001012663,0.0008765624,0.003488016,0.003147868],"category_scores_gemma":[0.00288161,0.0004734405,0.0004590295,0.0008051896,0.001103657,0.0007972635,0.0006309271,0.001819823,0.0005005302],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005100376,"about_ca_system_score_gemma":0.0004448716,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001029221,"about_ca_topic_score_gemma":0.0008196645,"domain_scores_codex":[0.9995806,0.00009442183,0.00004873991,0.00005714491,0.00006673764,0.0001524421],"domain_scores_gemma":[0.9990016,0.0004237839,0.000243942,0.00005529514,0.00004689813,0.0002285518],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0002741284,0.00004362159,0.03792227,0.00004489137,0.00001522442,0.9578078,0.00007580004,0.00008575642,0.0008491246,0.0003532365,0.0004402525,0.002087883],"study_design_scores_gemma":[0.00004097668,0.0001588594,0.0251668,0.00003471817,0.00004211472,0.9721217,0.00012099,0.0006662164,0.0005503455,0.0005222551,0.0005648591,0.00001024108],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9673823,0.006294183,0.001729409,0.003532403,0.0002586748,0.0001187171,0.0001191317,0.0001081715,0.02045704],"genre_scores_gemma":[0.9975716,0.0007040962,0.0003482466,0.0004231465,0.0005178576,0.0000083289,0.00003508832,0.000005530177,0.0003860107],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003488016,"threshold_uncertainty_score":0.01053065,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02682117618270937,"score_gpt":0.3002230536651932,"score_spread":0.2734018774824838,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}