{"id":"W3008020523","doi":"10.1016/j.visres.2020.01.006","title":"Transient pupillary light reflex in CEP290- or NPHP5-associated Leber congenital amaurosis: Latency as a potential outcome measure of cone function","year":2020,"lang":"en","type":"article","venue":"Vision Research","topic":"Retinal Development and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":15,"is_retracted":false,"has_abstract":false,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"National Eye Institute; Research to Prevent Blindness","keywords":"Stimulus (psychology); Ophthalmology; Audiology; Pupillary light reflex; Electroretinography; Pupillary response; Pupillary reflex; Reflex; Physics; Medicine; Neuroscience; Psychology; Optics; Pupil; Retinal","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006705684,0.0002593105,0.0003001444,0.0007788827,0.0001640945,0.0003861672,0.0002150853,0.0003954415,0.001566112],"category_scores_gemma":[0.002503511,0.00009473685,0.0001816978,0.0003159657,0.0003588413,0.0006317195,0.0003358375,0.0005771368,0.0003123521],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004386308,"about_ca_system_score_gemma":0.0002673168,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001891747,"about_ca_topic_score_gemma":0.001299418,"domain_scores_codex":[0.9996076,0.00009747442,0.00005533602,0.00006597179,0.00009142853,0.00008222593],"domain_scores_gemma":[0.9982805,0.0007188588,0.0003786117,0.00007910826,0.0001751706,0.0003678583],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.01352351,0.0004976796,0.6102582,0.0001633405,0.0001102709,0.01093174,0.0005037638,0.00103914,0.3329625,0.0005546986,0.0003361385,0.02911912],"study_design_scores_gemma":[0.00005616471,0.003237739,0.9364291,0.00001343037,0.0000772796,0.007954888,0.0003455159,0.002682638,0.04853186,0.0002609508,0.0003872675,0.00002319206],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9974527,0.0001588604,0.001032489,0.00002270518,0.000008573224,0.00001536359,0.0001737618,0.00002857471,0.001107009],"genre_scores_gemma":[0.999501,0.00003544449,0.0001310709,0.000009439301,0.000003351408,0.0000073472,0.0001035383,0.000007016044,0.0002018785],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001891747,"threshold_uncertainty_score":0.005239189,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05381034432943232,"score_gpt":0.3569141497006333,"score_spread":0.303103805371201,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}