{"id":"W3029145961","doi":"10.1017/cjn.2020.114","title":"Poor Yield of Routine Transthyretin Screening in Patients with Idiopathic Neuropathy","year":2020,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Amyloidosis: Diagnosis, Treatment, Outcomes","field":"Biochemistry, Genetics and Molecular Biology","cited_by":7,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University","funders":"Alnylam Pharmaceuticals","keywords":"Transthyretin; Medicine; Polyneuropathy; Amyloid polyneuropathy; Population; Genetic heterogeneity; Amyloidosis; Cohort; Internal medicine; Phenotype; Gene; Age of onset; Genetics; Disease; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001119639,0.0003038186,0.0003521894,0.0006989341,0.0005011855,0.000724795,0.0005314899,0.0006930471,0.001380838],"category_scores_gemma":[0.01182721,0.0001596281,0.0001870708,0.0005531745,0.0005053491,0.0004563098,0.0003992291,0.0004991745,0.0003804327],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006911409,"about_ca_system_score_gemma":0.0009534545,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01119003,"about_ca_topic_score_gemma":0.008787798,"domain_scores_codex":[0.9988425,0.0003418985,0.0001364449,0.0001648374,0.0003175919,0.0001966906],"domain_scores_gemma":[0.9931947,0.003130636,0.001487387,0.0003427206,0.001101727,0.0007427635],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00007381099,0.00002074404,0.9952591,0.00001049619,0.000007047027,0.0004954323,0.0001088934,0.00005067298,0.0001778234,0.00001412108,0.0001777818,0.00360411],"study_design_scores_gemma":[0.000008927368,0.0001549271,0.9941176,0.00002400532,0.00003405294,0.00391104,0.0004219611,0.0006119655,0.0002977377,0.00007344136,0.0003373612,0.000006927319],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9970476,0.0006198325,0.0001616483,0.0003517531,0.00001459516,0.00001219747,0.000143266,0.00002094718,0.001628172],"genre_scores_gemma":[0.9996351,0.00009655292,0.00006724383,0.00006668086,0.00001314985,0.000003344118,0.00006855383,0.000002085764,0.00004725419],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01119003,"threshold_uncertainty_score":0.02224976,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02259700433211832,"score_gpt":0.2334577080257563,"score_spread":0.210860703693638,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}