{"id":"W3030921368","doi":"10.4274/jcrpe.galenos.2020.2020.0094","title":"Hypophosphatasia: The Unusual Presentation","year":2020,"lang":"en","type":"letter","venue":"Journal of Clinical Research in Pediatric Endocrinology","topic":"Alkaline Phosphatase Research Studies","field":"Medicine","cited_by":2,"is_retracted":false,"has_abstract":false,"ca_institutions":"Stollery Children's Hospital; University of Alberta","funders":"","keywords":"Hypophosphatasia; Presentation (obstetrics); Medicine; Chemistry; Surgery; Biochemistry; Alkaline phosphatase; Enzyme","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008406723,0.002357444,0.001742159,0.002585578,0.002563732,0.002478354,0.002015974,0.02059767,0.003960513],"category_scores_gemma":[0.009860433,0.001270927,0.001618003,0.001897988,0.002095953,0.003927588,0.001345545,0.01100585,0.002095527],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.003224251,"about_ca_system_score_gemma":0.00137206,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002599513,"about_ca_topic_score_gemma":0.002609037,"domain_scores_codex":[0.9988428,0.0003168865,0.0001460616,0.000252143,0.0001769131,0.0002650702],"domain_scores_gemma":[0.9974994,0.0009694444,0.0003416803,0.0001402191,0.0002657911,0.0007835085],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00004653247,0.00003210928,0.00275236,0.00002725662,0.000006883066,0.9862968,0.00006872274,0.0001214977,0.0002602992,0.0008961507,0.008220992,0.001270438],"study_design_scores_gemma":[0.00003934608,0.00005393813,0.002172529,0.00005350123,0.00001226156,0.9900516,0.0001700287,0.0007710098,0.0001782659,0.001963807,0.004511886,0.00002182101],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"commentary","genre_gemma":"empirical","genre_scores_codex":[0.2266269,0.01971387,0.005076816,0.5928295,0.03091834,0.0002902995,0.000783651,0.0006895918,0.1230711],"genre_scores_gemma":[0.7925807,0.008189974,0.004552397,0.08740981,0.09357417,0.0001305992,0.0002836917,0.0001535691,0.01312513],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.02059767,"threshold_uncertainty_score":0.02339369,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.3362579302469039,"score_gpt":0.5487380188533106,"score_spread":0.2124800886064067,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}