{"id":"W3032620655","doi":"10.1093/jnen/nlaa045","title":"Expanding the Phenotype of Frontotemporal Lobar Degeneration With FUS-Positive Pathology (FTLD-FUS)","year":2020,"lang":"en","type":"article","venue":"Journal of Neuropathology & Experimental Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":9,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Alberta; University of British Columbia","funders":"Canadian Institutes of Health Research","keywords":"Frontotemporal lobar degeneration; Pathology; Phenotype; Medicine; Degeneration (medical); Frontotemporal dementia; Biology; Disease; Dementia; Gene; Genetics","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002580111,0.00103085,0.0004054043,0.001006373,0.0006630711,0.0004056061,0.0004220616,0.0008138159,0.001572899],"category_scores_gemma":[0.001066157,0.0002038357,0.0003740772,0.0005966332,0.0008608031,0.0006783323,0.001014267,0.0004676912,0.0007292068],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002434521,"about_ca_system_score_gemma":0.0002938031,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001857212,"about_ca_topic_score_gemma":0.001905446,"domain_scores_codex":[0.9998337,0.00001623682,0.00001986606,0.0000431237,0.00003211342,0.00005493259],"domain_scores_gemma":[0.999674,0.00009455717,0.00009078518,0.00003889095,0.00003505947,0.00006674598],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.0001584069,0.0001100802,0.0660258,0.0001094769,0.00002020899,0.8700709,0.001231289,0.0003775281,0.03529837,0.0009316883,0.0006440668,0.02502215],"study_design_scores_gemma":[0.000008759538,0.000111016,0.03474187,0.00001448238,0.00001553303,0.9601055,0.0001535623,0.0003468425,0.003109848,0.0004862831,0.0008950467,0.00001124707],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9868156,0.0006216108,0.002998008,0.0001184539,0.00002999846,0.00005836504,0.0001213145,0.0001155466,0.009121161],"genre_scores_gemma":[0.9980235,0.0001759593,0.0009481225,0.00009413216,0.00003532041,0.00001162757,0.0000668167,0.00001303553,0.0006314951],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001857212,"threshold_uncertainty_score":0.005261898,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02990201357212828,"score_gpt":0.2944380356241164,"score_spread":0.2645360220519881,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}