{"id":"W3038629602","doi":"10.1111/jth.14990","title":"A new pedigree with thrombomodulin‐associated coagulopathy in which delayed fibrinolysis is partially attenuated by co‐inherited TAFI deficiency","year":2020,"lang":"en","type":"article","venue":"Journal of Thrombosis and Haemostasis","topic":"Blood Coagulation and Thrombosis Mechanisms","field":"Medicine","cited_by":24,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Medical Research Council; NIHR BioResource; Vlaamse regering; University of Aberdeen; Fonds Wetenschappelijk Onderzoek; University of Bristol; Department of Health and Social Care; British Heart Foundation; Universiteit Antwerpen; National Institute for Health and Care Research; Medical Research Council Canada; NHS Blood and Transplant","keywords":"Thrombomodulin; Fibrinolysis; Coagulopathy; Thrombin; Immunology; Hemostasis; Coagulation; Medicine; Protein C; Biology; Internal medicine; Platelet","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003371075,0.001850008,0.0006628074,0.001621353,0.001372371,0.0006141057,0.0006220129,0.001238366,0.002219886],"category_scores_gemma":[0.002124114,0.000613371,0.0005859801,0.001006978,0.0008132588,0.0004397742,0.000788193,0.001264249,0.0002744502],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004628137,"about_ca_system_score_gemma":0.0003995845,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003995674,"about_ca_topic_score_gemma":0.00360387,"domain_scores_codex":[0.9994561,0.0001108472,0.00005847448,0.000211601,0.00009048805,0.000072496],"domain_scores_gemma":[0.9989613,0.0003293466,0.0002070547,0.00007947591,0.00009397204,0.0003287572],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.0003319436,0.0003052531,0.09545233,0.0001015925,0.0001411584,0.875303,0.001624041,0.00052433,0.01326796,0.00103956,0.00188417,0.01002468],"study_design_scores_gemma":[0.00005383906,0.0002934937,0.04478523,0.00003103424,0.00007245874,0.9505042,0.0001901384,0.0009296264,0.001039914,0.0004487494,0.001617383,0.00003399187],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9912586,0.0005199324,0.004568429,0.000836875,0.00009071123,0.00009137022,0.000581279,0.0001152873,0.001937414],"genre_scores_gemma":[0.99632,0.0002645258,0.002067753,0.0002276409,0.0001018106,0.00001590347,0.0002633986,0.00001863826,0.0007203327],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003995674,"threshold_uncertainty_score":0.007944882,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05427822538908811,"score_gpt":0.3029623565187844,"score_spread":0.2486841311296963,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}