{"id":"W3041730227","doi":"10.1007/s10875-020-00814-6","title":"Neuroinflammatory Disease as an Isolated Manifestation of Hemophagocytic Lymphohistiocytosis","year":2020,"lang":"en","type":"review","venue":"Journal of Clinical Immunology","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":83,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Toronto; Hospital for Sick Children; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"Deutsche Kinderkrebsstiftung; Bundesministerium für Bildung und Forschung; Deutsche Forschungsgemeinschaft","keywords":"Hemophagocytic lymphohistiocytosis; Medicine; Acute disseminated encephalomyelitis; Pediatrics; Leukoencephalopathy; Cytopenia; Ataxia; Encephalopathy; Neurology; Internal medicine; Disease; Bone marrow","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003433267,0.0008873233,0.001481441,0.002298542,0.0001984782,0.0008616606,0.0007588277,0.0009389566,0.00170235],"category_scores_gemma":[0.0006955916,0.0002412919,0.0003388358,0.001938677,0.0004900465,0.001087253,0.0005151706,0.001371828,0.001177451],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003862557,"about_ca_system_score_gemma":0.0008939352,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001099695,"about_ca_topic_score_gemma":0.002383427,"domain_scores_codex":[0.9998302,0.0000262,0.00003798142,0.00003277833,0.00005272212,0.00002009126],"domain_scores_gemma":[0.9996682,0.0001555233,0.00007154301,0.000008355945,0.00006184957,0.00003448967],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001268937,0.00005722314,0.0009838169,0.01298636,0.0001395422,0.003808809,0.00005334602,0.0002112133,0.001653816,0.001412573,0.03478139,0.9437851],"study_design_scores_gemma":[0.00008265223,0.0001435788,0.006977738,0.01390493,0.00073123,0.05776656,0.0001960643,0.0002488276,0.001032576,0.00294042,0.9158923,0.00008301966],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001861488,0.9984539,0.00009404271,0.0002056163,0.0002057424,0.000002862565,0.00001128958,0.000005494161,0.0008349198],"genre_scores_gemma":[0.00176839,0.9967148,0.0001641804,0.0003622477,0.0005635346,0.000003405844,0.00003003975,0.000001218807,0.0003921589],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.002298542,"threshold_uncertainty_score":0.005694866,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1059150168073805,"score_gpt":0.4624335376575035,"score_spread":0.356518520850123,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}