{"id":"W3043816786","doi":"10.3390/jcm9072234","title":"Hereditary ATTR Amyloidosis in Austria: Prevalence and Epidemiological Hot Spots","year":2020,"lang":"en","type":"article","venue":"Journal of Clinical Medicine","topic":"Amyloidosis: Diagnosis, Treatment, Outcomes","field":"Biochemistry, Genetics and Molecular Biology","cited_by":21,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Toronto","funders":"Oesterreichische Nationalbank","keywords":"Medicine; Epidemiology; Amyloidosis; Pediatrics; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005900518,0.0001439407,0.0002560508,0.001713195,0.0002183792,0.0005696043,0.0001660711,0.0003508658,0.001347864],"category_scores_gemma":[0.001011088,0.0001596092,0.0001950947,0.0009103869,0.0002544267,0.0003107112,0.0004143131,0.0001916148,0.0003056501],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002301409,"about_ca_system_score_gemma":0.0001838768,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009576583,"about_ca_topic_score_gemma":0.0008173776,"domain_scores_codex":[0.9996065,0.0001076463,0.00005688952,0.000104327,0.00007275947,0.00005185395],"domain_scores_gemma":[0.9991862,0.0001686626,0.000388315,0.00004034125,0.000100633,0.0001158695],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00005671152,0.00002249583,0.9924219,0.00002109505,0.00002886859,0.0003425062,0.0001565379,0.00008706991,0.0007821766,0.00006934658,0.0001341351,0.005877062],"study_design_scores_gemma":[0.000003810643,0.00006257152,0.9962667,0.00001939263,0.00001925363,0.002441514,0.0002913194,0.0002366353,0.0001022087,0.00008755915,0.0004648717,0.000004258578],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9980733,0.0008521705,0.0002117039,0.00005292896,0.000006966946,0.000004788499,0.0001441793,0.000007548857,0.0006462871],"genre_scores_gemma":[0.9994198,0.0002977905,0.0001158276,0.00001441331,0.00000763435,0.000002645211,0.00009230638,0.000001137046,0.00004845961],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001713195,"threshold_uncertainty_score":0.004509091,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.109157801470824,"score_gpt":0.4092086635246228,"score_spread":0.3000508620537987,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}