{"id":"W3047665105","doi":"10.1016/j.xkme.2020.05.014","title":"Alport Syndrome Classification and Management","year":2020,"lang":"en","type":"review","venue":"Kidney Medicine","topic":"Cell Adhesion Molecules Research","field":"Medicine","cited_by":97,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"National Institutes of Health; Vertex Pharmaceuticals; AbbVie; Boehringer Ingelheim; Amgen; Baxter Healthcare Corporation; Nurses Organization of Veterans Affairs; Bristol-Myers Squibb; AstraZeneca; Gilead Sciences; Daiichi Sankyo Company; Alport Syndrome Foundation; U.S. Department of Veterans Affairs","keywords":"Alport syndrome; Focal segmental glomerulosclerosis; Inflammation; Kidney disease; Medicine; Glomerular basement membrane; Glomerulonephritis; Nephropathy; Immunology; Proinflammatory cytokine; Minimal change disease; Population; Kidney; Pathology; Internal medicine; Endocrinology; Diabetes mellitus","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007077047,0.0005943187,0.000741937,0.002366122,0.001075901,0.001050217,0.0009149924,0.0008633586,0.008573104],"category_scores_gemma":[0.002119836,0.0001150634,0.0004984268,0.001936825,0.0002971315,0.0006963133,0.0008732728,0.001067461,0.001857866],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0009567432,"about_ca_system_score_gemma":0.001392485,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006153508,"about_ca_topic_score_gemma":0.003525715,"domain_scores_codex":[0.9992179,0.0001240665,0.0001498711,0.0001115591,0.0002737813,0.000122946],"domain_scores_gemma":[0.9993418,0.00005348039,0.0001936947,0.00001957753,0.0002528584,0.0001385269],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.000409696,0.0002854021,0.3294335,0.001182973,0.0001847424,0.01419277,0.001061505,0.0009136004,0.001992663,0.00917547,0.2848912,0.3562766],"study_design_scores_gemma":[0.0002181989,0.0003164181,0.352539,0.008036324,0.0002764149,0.1375759,0.001805471,0.003518969,0.0009211055,0.01427142,0.480362,0.0001588973],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"other","genre_gemma":"review","genre_scores_codex":[0.3014451,0.2634201,0.02868421,0.03799259,0.004598307,0.003620345,0.02396675,0.00163092,0.3346417],"genre_scores_gemma":[0.7591494,0.1106754,0.02459795,0.01192739,0.004450924,0.00262824,0.04723408,0.0003476144,0.03898902],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.008573104,"threshold_uncertainty_score":0.02867991,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1102278547027897,"score_gpt":0.4018705233406457,"score_spread":0.2916426686378559,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}