{"id":"W3087294558","doi":"10.1155/2020/8489707","title":"Clinical Course and Nutritional Management of Propionic and Methylmalonic Acidemias","year":2020,"lang":"en","type":"article","venue":"Journal of Nutrition and Metabolism","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":6,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"BC Children's Hospital","keywords":"Medicine; Methylmalonic acidemia; Intensive care medicine; Pediatrics","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002432867,0.0001769256,0.0001972819,0.0007337543,0.0002909584,0.0003831319,0.0002054076,0.000252448,0.0007477098],"category_scores_gemma":[0.00190213,0.000114637,0.0001671533,0.0006368764,0.000179454,0.000337877,0.0002537353,0.0003187669,0.0001300739],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003832927,"about_ca_system_score_gemma":0.0004428506,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003292615,"about_ca_topic_score_gemma":0.003154979,"domain_scores_codex":[0.9997683,0.00004852216,0.00006085591,0.00003235594,0.00004326852,0.00004670115],"domain_scores_gemma":[0.9994751,0.00007345738,0.0002912961,0.00001101441,0.00006494583,0.00008421673],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001693232,0.00003917941,0.9809301,0.00006412202,0.000030112,0.009482077,0.0001290491,0.00005795335,0.0005964984,0.00005051398,0.0002051302,0.008245918],"study_design_scores_gemma":[0.00001011145,0.0001837404,0.9596403,0.0001376381,0.00003302615,0.03771503,0.0007799926,0.0002231673,0.0003569822,0.0001032962,0.0008092413,0.000007511666],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9925401,0.004636514,0.0002497419,0.0002360989,0.00001228309,0.0000275248,0.0002546396,0.000006629719,0.00203655],"genre_scores_gemma":[0.9977697,0.001537674,0.0001772365,0.00007072945,0.00001403076,0.000008552425,0.0002149076,0.000001681194,0.0002054772],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003292615,"threshold_uncertainty_score":0.006546915,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02202719268079196,"score_gpt":0.3117401025914401,"score_spread":0.2897129099106481,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}