{"id":"W3087294558","doi":"10.1155/2020/8489707","title":"Clinical Course and Nutritional Management of Propionic and Methylmalonic Acidemias","year":2020,"lang":"en","type":"article","venue":"Journal of Nutrition and Metabolism","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":6,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"BC Children's Hospital","keywords":"Medicine; Methylmalonic acidemia; Intensive care medicine; Pediatrics","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004019337,0.0001020622,0.0003003929,0.00003629237,0.00003363537,0.00001479961,0.0000691514,0.00009354158,0.00001077599],"category_scores_gemma":[0.00004823811,0.00008662117,0.00008913495,0.00006002749,0.0001515293,0.00001024,0.00006366117,0.0001103246,3.451442e-7],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":5.564085e-7,"about_ca_system_score_gemma":0.00003081008,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":5.841476e-7,"about_ca_topic_score_gemma":3.474408e-7,"domain_scores_codex":[0.9990171,0.0001049544,0.0004592596,0.0001695887,0.000147271,0.0001018302],"domain_scores_gemma":[0.9993672,0.00001850205,0.0002329337,0.00007299412,0.0001200487,0.0001882573],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00478373,0.005675244,0.03503732,0.005317028,0.004232686,0.0001411305,0.0009598128,0.0000213142,0.2747193,0.04136603,0.0477241,0.5800223],"study_design_scores_gemma":[0.01698835,0.000818141,0.299237,0.0002363984,0.0009101874,0.0003330598,0.001187903,0.00005008112,0.009995278,0.00393083,0.6659511,0.0003616383],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8911753,0.1053175,0.0006236664,0.002484764,0.0001319415,0.000158052,0.00001734977,0.000001844501,0.00008956224],"genre_scores_gemma":[0.8552344,0.1336317,0.009993892,0.0007231048,0.0003615196,0.000004761511,0.000009946786,0.000008654802,0.00003202818],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6182271,"threshold_uncertainty_score":0.3532309,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02202719268079196,"score_gpt":0.3117401025914401,"score_spread":0.2897129099106481,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}