{"id":"W3089672552","doi":"10.3899/jrheum.191274","title":"The Storm Beneath the Storm: MAS-HLH in Inflammatory Myopathies","year":2020,"lang":"en","type":"letter","venue":"The Journal of Rheumatology","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"National Institute of Arthritis and Musculoskeletal and Skin Diseases","keywords":"Medicine; Macrophage activation syndrome; Dermatomyositis; Polymyositis; Rheumatology; Juvenile dermatomyositis; Hemophagocytic lymphohistiocytosis; Internal medicine; Arthritis; Disease; Hemophagocytosis; Immunology; Pediatrics","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007475149,0.000366254,0.0006442008,0.002271657,0.000735386,0.00139535,0.0005819982,0.001207518,0.001002261],"category_scores_gemma":[0.002530146,0.0002845057,0.0002522601,0.002746153,0.0005642758,0.001333104,0.0009525805,0.001006757,0.0003432025],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003699543,"about_ca_system_score_gemma":0.0004924614,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001061054,"about_ca_topic_score_gemma":0.001813059,"domain_scores_codex":[0.999403,0.00007925615,0.0001491161,0.000100522,0.000150615,0.0001174862],"domain_scores_gemma":[0.9980757,0.0005286069,0.0006190585,0.000103803,0.000242771,0.0004300412],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0001677018,0.0000868458,0.9293697,0.0001226258,0.00002829717,0.03610292,0.0007490718,0.0001318517,0.0009089279,0.0004279177,0.003782459,0.0281217],"study_design_scores_gemma":[0.00004153244,0.0002201212,0.702283,0.0004347939,0.0001203165,0.2798934,0.002853506,0.001014992,0.0006211663,0.0009497891,0.01152282,0.00004463649],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"commentary","genre_scores_codex":[0.9640583,0.02511448,0.001537566,0.005468063,0.0006081123,0.00006743464,0.000288053,0.00004596859,0.002812119],"genre_scores_gemma":[0.9869665,0.007372425,0.001014644,0.001342289,0.002687925,0.00002029573,0.0002516565,0.00001318457,0.0003310657],"genre_candidate":"commentary","genre_consensus":null,"teacher_disagreement_score":0.002271657,"threshold_uncertainty_score":0.003953278,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01975758525246219,"score_gpt":0.2675676145954175,"score_spread":0.2478100293429553,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}