{"id":"W3093626132","doi":"10.1111/epi.16684","title":"Starting stiripentol in adults with Dravet syndrome? Watch for ammonia and carnitine","year":2020,"lang":"en","type":"article","venue":"Epilepsia","topic":"Epilepsy research and treatment","field":"Medicine","cited_by":24,"is_retracted":false,"has_abstract":true,"ca_institutions":"Toronto Western Hospital; University of Toronto; University Health Network","funders":"Dravet Syndrome Foundation","keywords":"Dravet syndrome; Medicine; Carnitine; Encephalopathy; Epilepsy; Pediatrics; Population; Confidence interval; Internal medicine; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001270763,0.0001574813,0.0003388746,0.00004788055,0.0000557183,0.00002184452,0.0000501904,0.00004808369,0.00006256533],"category_scores_gemma":[0.0001668748,0.0001159179,0.00003860157,0.0001860779,0.00005935458,0.00006747177,0.00003513831,0.0001887264,0.00002351378],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004823416,"about_ca_system_score_gemma":0.00008169616,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00016846,"about_ca_topic_score_gemma":0.0001706539,"domain_scores_codex":[0.9987628,0.00003133326,0.0002225618,0.0003455524,0.0002340371,0.0004037486],"domain_scores_gemma":[0.9992507,0.0001129125,0.00004816695,0.0001454092,0.00006954816,0.0003733326],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.003646234,0.0002058178,0.9834704,0.0006608322,0.0001104237,0.001509189,0.001811798,0.000005086816,0.0003209938,0.0001322844,0.001832129,0.00629479],"study_design_scores_gemma":[0.02453371,0.01084706,0.95143,0.001165386,0.0001405958,0.0001861381,0.00153464,0.003996569,0.001743288,0.0002154206,0.003825533,0.0003816391],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9839618,0.0002605586,0.0001255115,0.01381925,0.00001367167,0.001209867,0.00003661617,0.00004750482,0.0005252108],"genre_scores_gemma":[0.9955153,0.00005742261,0.003293236,0.0005583462,0.00006426575,0.0001612298,0.0000860881,0.00002879476,0.000235355],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0320404,"threshold_uncertainty_score":0.4726995,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02066519728204228,"score_gpt":0.2756805227693591,"score_spread":0.2550153254873168,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}