{"id":"W3124216015","doi":"10.1017/cjn.2021.12","title":"Infantile Spasms and Trisomy 21: Unfavorable Outcomes with First-line Vigabatrin Therapy","year":2021,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Epilepsy research and treatment","field":"Medicine","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital; University of British Columbia","funders":"","keywords":"Vigabatrin; Etiology; Epileptic spasms; Medicine; Epilepsy; Trisomy; Pediatrics; Retrospective cohort study; Generalized epilepsy; Internal medicine; Anticonvulsant; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004531041,0.000207544,0.000405673,0.0006310591,0.0004116448,0.0004197531,0.0001756235,0.0003688693,0.001313728],"category_scores_gemma":[0.0022035,0.00009122071,0.0004235168,0.0005169641,0.0003900001,0.0003607798,0.0004269099,0.0004723445,0.0001893468],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000286958,"about_ca_system_score_gemma":0.0003970095,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001268047,"about_ca_topic_score_gemma":0.001416222,"domain_scores_codex":[0.9995567,0.0001033694,0.0000612116,0.00006949181,0.00009017478,0.0001189801],"domain_scores_gemma":[0.9970047,0.0004402753,0.001824091,0.00009403042,0.0001200067,0.0005167811],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004326115,0.00003168999,0.9956682,0.000008012439,0.00003319053,0.0009761066,0.00003302417,0.0000368626,0.0002245873,0.0000138365,0.00002984831,0.002512131],"study_design_scores_gemma":[0.00001091326,0.0003706074,0.9944038,0.00001017834,0.00002862359,0.004764758,0.0000995754,0.00007220606,0.0001150106,0.00002611198,0.00009440664,0.000003776741],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9990134,0.0003833925,0.00003605249,0.00002861511,0.000003835541,0.000004384747,0.00006092686,0.000002274844,0.0004670687],"genre_scores_gemma":[0.9996648,0.0001319584,0.00002115441,0.00001373007,0.00001152507,0.000003338436,0.0001087521,9.367124e-7,0.00004384655],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001313728,"threshold_uncertainty_score":0.004394829,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04000879846946404,"score_gpt":0.2990617626575845,"score_spread":0.2590529641881205,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}