{"id":"W3127282633","doi":"","title":"Familial Spastic Paraplegia and the ALS2 gene","year":2005,"lang":"en","type":"article","venue":"VUBIR (Vrije Universiteit Brussel)","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"SickKids Foundation; Hospital for Sick Children","funders":"","keywords":"Hereditary spastic paraplegia; Paraplegia; Spastic; Physical medicine and rehabilitation; Medicine; Gene; Genetics; Neuroscience; Biology; Spinal cord; Cerebral palsy; Phenotype","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001670069,0.0002421502,0.0002431191,0.0001168887,0.0003935844,0.00006227742,0.0005543802,0.0001047764,0.0004458857],"category_scores_gemma":[0.0004366007,0.0001760112,0.0001073425,0.0004141855,0.000807313,0.0003653761,0.0002450474,0.0003159266,0.0004409996],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003722792,"about_ca_system_score_gemma":0.00003906083,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00008547828,"about_ca_topic_score_gemma":0.00005045021,"domain_scores_codex":[0.9980913,0.0003069623,0.000192842,0.0005990012,0.0003325832,0.0004772529],"domain_scores_gemma":[0.9985566,0.0007749996,0.00007894726,0.0003809422,0.00002596994,0.0001825637],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"not_applicable","study_design_scores_codex":[0.008907287,0.00139239,0.004697068,0.0001425157,0.0002275225,0.003484954,0.01103966,0.01173416,0.5551197,0.1997368,0.06404713,0.1394708],"study_design_scores_gemma":[0.02705866,0.001492945,0.03086121,0.00004714091,0.0004636771,0.0007461652,0.002374759,0.05239128,0.05833337,0.007547902,0.8161209,0.002561952],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9739569,0.0001980226,0.0003142759,0.009179025,0.0002421037,0.0004082256,0.00003389391,0.0002228441,0.01544474],"genre_scores_gemma":[0.9925861,0.0003405827,0.0002202275,0.005651318,0.0002388891,0.000002681459,0.00000277273,0.00002196097,0.0009354478],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.7520738,"threshold_uncertainty_score":0.7177529,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01496664248615055,"score_gpt":0.2023663442337945,"score_spread":0.1873997017476439,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}