{"id":"W3127282633","doi":"","title":"Familial Spastic Paraplegia and the ALS2 gene","year":2005,"lang":"en","type":"article","venue":"VUBIR (Vrije Universiteit Brussel)","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"SickKids Foundation; Hospital for Sick Children","funders":"","keywords":"Hereditary spastic paraplegia; Paraplegia; Spastic; Physical medicine and rehabilitation; Medicine; Gene; Genetics; Neuroscience; Biology; Spinal cord; Cerebral palsy; Phenotype","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002336593,0.00119567,0.0005206036,0.001095112,0.0007622438,0.0003997868,0.000323197,0.001284112,0.004153056],"category_scores_gemma":[0.0008013346,0.0003192961,0.0002761105,0.000905399,0.0006299522,0.0002543787,0.000599156,0.0004372014,0.0003765664],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005046945,"about_ca_system_score_gemma":0.0004337923,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005874028,"about_ca_topic_score_gemma":0.004865681,"domain_scores_codex":[0.9997098,0.00009662084,0.00002720297,0.00005912078,0.00004761674,0.00005963063],"domain_scores_gemma":[0.9996892,0.0001185848,0.00007276153,0.00001507877,0.00002479142,0.00007954588],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.004211079,0.0004524511,0.1050677,0.0002780073,0.0003996195,0.8141264,0.0009580771,0.001007266,0.05044883,0.00374552,0.003797629,0.01550735],"study_design_scores_gemma":[0.0005413447,0.0008204515,0.3507491,0.0002298225,0.0004565965,0.6247578,0.0006500193,0.002154397,0.008252368,0.004071409,0.007245765,0.00007089275],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.987883,0.003391302,0.0005386569,0.0007688942,0.00006477742,0.00001366176,0.0003032036,0.00004004046,0.006996362],"genre_scores_gemma":[0.9970648,0.000524952,0.0002336378,0.0001275517,0.0000688672,0.000006231433,0.000145301,0.000009165014,0.001819597],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005874028,"threshold_uncertainty_score":0.01389331,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01496664248615055,"score_gpt":0.2023663442337945,"score_spread":0.1873997017476439,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}