{"id":"W3127311419","doi":"10.1002/mds.28519","title":"Brain Damage and Gene Expression Across Hereditary Spastic Paraplegia Subtypes","year":2021,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":28,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Calgary","funders":"Coordenação de Aperfeiçoamento de Pessoal de Nível Superior; Fundação de Amparo à Pesquisa do Estado de São Paulo","keywords":"Hereditary spastic paraplegia; Cerebellum; White matter; Pathology; Neuroscience; Atrophy; Biology; Medicine; Gene; Genetics; Phenotype; Magnetic resonance imaging","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003051563,0.0003213017,0.000238383,0.001096932,0.0002329132,0.0003810581,0.00018429,0.0002799084,0.001468522],"category_scores_gemma":[0.0007171151,0.0001231569,0.000247256,0.0007923009,0.0002897283,0.0001529031,0.0003843413,0.0001684846,0.0002050174],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001594656,"about_ca_system_score_gemma":0.00009434378,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001569454,"about_ca_topic_score_gemma":0.002503425,"domain_scores_codex":[0.9998172,0.0000223286,0.00001974668,0.00008401433,0.00003043996,0.00002627183],"domain_scores_gemma":[0.9995505,0.00005777907,0.000228078,0.00004071279,0.00005687249,0.00006601409],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004882083,0.00002797056,0.9776374,0.00003949612,0.0002650182,0.0004440679,0.0002339578,0.000248696,0.01594419,0.00005657601,0.0001836172,0.004430776],"study_design_scores_gemma":[0.00000254411,0.00003774078,0.9988023,0.00000467668,0.00002544397,0.0005028899,0.0000575087,0.0001226361,0.0003322042,0.00004284657,0.00006772349,0.00000142591],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9993634,0.00008580357,0.00007821927,0.000006882859,7.078278e-7,0.000002979973,0.0003223139,0.00000389579,0.0001358176],"genre_scores_gemma":[0.9991359,0.0000582913,0.0001105328,0.000006389753,0.000001633034,0.000005923232,0.0005944522,0.00000370312,0.00008315006],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001569454,"threshold_uncertainty_score":0.004912674,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02029166962296234,"score_gpt":0.2655924063095929,"score_spread":0.2453007366866306,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}