{"id":"W3130260427","doi":"10.3389/fneur.2021.642228","title":"Treat Iron-Related Childhood-Onset Neurodegeneration (TIRCON)—An International Network on Care and Research for Patients With Neurodegeneration With Brain Iron Accumulation (NBIA)","year":2021,"lang":"en","type":"review","venue":"Frontiers in Neurology","topic":"Neurological diseases and metabolism","field":"Neuroscience","cited_by":8,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Neurodegeneration; Medicine; Neuroscience; Pediatrics; Psychology; Pathology; Disease","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.02996446,0.001020352,0.0007962753,0.002180288,0.002291942,0.00472131,0.004066984,0.003042418,0.01028476],"category_scores_gemma":[0.01824953,0.0004506228,0.001535797,0.002172816,0.002225576,0.003621446,0.01289406,0.005770116,0.006242687],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00694301,"about_ca_system_score_gemma":0.03783833,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.011203,"about_ca_topic_score_gemma":0.01634181,"domain_scores_codex":[0.9893477,0.004330558,0.0009414837,0.001492979,0.002217672,0.001669612],"domain_scores_gemma":[0.948756,0.005987382,0.005308379,0.004640796,0.01243871,0.02286886],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0009225069,0.0005228249,0.01889194,0.001100602,0.0002787854,0.0007813598,0.001619468,0.001003112,0.00338598,0.03087547,0.5661899,0.374428],"study_design_scores_gemma":[0.0004414042,0.0007574696,0.02053497,0.00221072,0.0002118495,0.001237225,0.0009842286,0.001207574,0.001815209,0.006207955,0.9643092,0.00008222286],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"review","genre_scores_codex":[0.05494644,0.09157266,0.0695736,0.4341934,0.01932391,0.00736715,0.01568171,0.005817113,0.301524],"genre_scores_gemma":[0.271118,0.06722092,0.2530698,0.1812594,0.01382708,0.01519588,0.05819291,0.00401842,0.1360975],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.02996446,"threshold_uncertainty_score":0.1584691,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06100709811602718,"score_gpt":0.3575222455272937,"score_spread":0.2965151474112666,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}