{"id":"W3150796527","doi":"10.4021/jmc221w","title":"Rapidly Progressive Creutzfeldt-Jakob Disease VV1 Subtype","year":2011,"lang":"en","type":"article","venue":"Journal of Medical Cases","topic":"Prion Diseases and Protein Misfolding","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Medicine; Brain biopsy; Pathology; Dementia; Disease; Magnetic resonance imaging; Creutzfeldt-Jakob Syndrome; Encephalopathy; Personality changes; Prion protein; Internal medicine; Radiology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001870067,0.000548979,0.0002636759,0.0006129523,0.0006187411,0.0004665938,0.0003727454,0.0006924628,0.001577348],"category_scores_gemma":[0.0008266719,0.0001888657,0.0002377148,0.0002774077,0.0003690763,0.0003766707,0.0003157908,0.0004270021,0.0007799051],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003089271,"about_ca_system_score_gemma":0.0001694733,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001555817,"about_ca_topic_score_gemma":0.001502523,"domain_scores_codex":[0.9998456,0.00001964019,0.00001347708,0.0000311238,0.00004667653,0.00004339866],"domain_scores_gemma":[0.9998254,0.00002969967,0.00007391037,0.00001900365,0.00002036004,0.00003165175],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0004727734,0.0002211627,0.1894301,0.0003244907,0.00005045391,0.7318814,0.001357762,0.0002411975,0.03454089,0.00292407,0.004511597,0.03404401],"study_design_scores_gemma":[0.00002469743,0.0001580029,0.06544322,0.00004950515,0.00002829704,0.9221364,0.000220667,0.0003589522,0.004761565,0.0009951314,0.005807627,0.00001583235],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9834667,0.002821032,0.0009954214,0.0004431903,0.00006581294,0.00005705867,0.0001908604,0.00008100297,0.01187891],"genre_scores_gemma":[0.9968636,0.0006623358,0.0002943657,0.0001416241,0.00006036206,0.000003962562,0.00009162628,0.00001117993,0.001870973],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001577348,"threshold_uncertainty_score":0.00527674,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02909858416154289,"score_gpt":0.2979467325136756,"score_spread":0.2688481483521327,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}