{"id":"W3156053599","doi":"10.1016/j.ekir.2021.03.849","title":"POS-816 MAGNITUDE OF THE POTENTIAL SCREENING GAP FOR FABRY DISEASE IN MANITOBA, CANADA","year":2021,"lang":"en","type":"article","venue":"Kidney International Reports","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Manitoba; Seven Oaks General Hospital","funders":"","keywords":"Fabry disease; Medicine; Enzyme replacement therapy; Disease; Pediatrics; Internal medicine; Intensive care medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001742624,0.0004525949,0.0006170209,0.002005765,0.004107141,0.002153062,0.002008555,0.001253457,0.01252103],"category_scores_gemma":[0.004419347,0.0004980723,0.0007015524,0.002759015,0.00106105,0.0006437942,0.001650301,0.00176708,0.001183345],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.05443113,"about_ca_system_score_gemma":0.1794387,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.993938,"about_ca_topic_score_gemma":0.9973662,"domain_scores_codex":[0.997943,0.0003084834,0.0001332817,0.0001523532,0.0005849405,0.0008779883],"domain_scores_gemma":[0.9907521,0.0007751334,0.0004641097,0.0001268315,0.004498933,0.003382803],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003800196,0.0002760554,0.7478554,0.0008282358,0.0002087349,0.003238944,0.001835308,0.0009650671,0.002090858,0.007357485,0.1552966,0.07966738],"study_design_scores_gemma":[0.0001790575,0.0001369966,0.9147901,0.00164798,0.0001676345,0.001096612,0.007295484,0.002043648,0.00039448,0.00109993,0.07104737,0.000100715],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.5346547,0.03345301,0.002816164,0.2786523,0.002972262,0.001118853,0.05775346,0.0006362652,0.08794308],"genre_scores_gemma":[0.8845401,0.01635595,0.005862644,0.04401594,0.0003872324,0.0004711299,0.01140625,0.0001583895,0.03680232],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05443113,"threshold_uncertainty_score":0.3949273,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02470095232789199,"score_gpt":0.2884790677330967,"score_spread":0.2637781154052047,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}