{"id":"W3156317679","doi":"10.1002/mdc3.13218","title":"Cerebellar Ataxia in Adults with <scp><i>SQSTM1</i></scp>‐Associated Frontotemporal <scp>Dementia–Amyotrophic</scp> Lateral Sclerosis Spectrum of Disorders","year":2021,"lang":"en","type":"article","venue":"Movement Disorders Clinical Practice","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Psychology; Frontotemporal dementia; Fasciculation; Dysarthria; Dysmetria; Apathy; Neurological examination; Audiology; Physical medicine and rehabilitation; Blepharospasm; Executive dysfunction; Amyotrophic lateral sclerosis; Ataxia; Medicine; Dementia; Dystonia; Psychiatry; Neuroscience; Cognition; Internal medicine; Disease","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002352383,0.001046386,0.0005438321,0.001590871,0.001062158,0.0006612079,0.0003638644,0.0008253523,0.00217037],"category_scores_gemma":[0.0009366602,0.0003051248,0.0003469989,0.001406159,0.0006322402,0.0008843645,0.0006417787,0.0005485365,0.0005268747],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006140428,"about_ca_system_score_gemma":0.000521349,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.008282287,"about_ca_topic_score_gemma":0.01198503,"domain_scores_codex":[0.9997345,0.00002292559,0.00005181639,0.00006993068,0.00005068344,0.00007021878],"domain_scores_gemma":[0.9996418,0.00004423319,0.0001310749,0.000009961921,0.00005080713,0.0001221182],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003299587,0.0001276471,0.7583061,0.0001025627,0.00006305239,0.2266191,0.0006453538,0.0001749624,0.003272915,0.000248013,0.001345119,0.008765127],"study_design_scores_gemma":[0.00003456413,0.0004025258,0.7309465,0.0001022766,0.0001049294,0.2654776,0.0005929704,0.0004463184,0.0003506312,0.000307727,0.001213199,0.00002069135],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9884014,0.001920914,0.0003836938,0.0003916604,0.00003961699,0.00006732806,0.0002296392,0.00006463691,0.00850123],"genre_scores_gemma":[0.9987325,0.0004220784,0.0001208807,0.0001538818,0.00004463916,0.000006720545,0.0001511132,0.000003716425,0.0003643997],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.008282287,"threshold_uncertainty_score":0.01646811,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02645963063073476,"score_gpt":0.310014588409203,"score_spread":0.2835549577784683,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}