{"id":"W3157327845","doi":"10.1002/mds.28610","title":"Regional Brain and Spinal Cord Volume Loss in Spinocerebellar Ataxia Type 3","year":2021,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":59,"is_retracted":false,"has_abstract":true,"ca_institutions":"Western University","funders":"IXICO; Bundesministerium für Gesundheit; National Institute of Neurological Disorders and Stroke; Bundesministerium für Bildung und Forschung; Radboud Universiteit; ZonMw; Agence Nationale de la Recherche; National Institute of Biomedical Imaging and Bioengineering; E-Rare; EU Joint Programme – Neurodegenerative Disease Research; Medical Research Council; AveXis; Biogen; European Commission; Pfizer; Deutsche Forschungsgemeinschaft; Robert Bosch Stiftung; Hersenstichting; Eberhard Karls Universität Tübingen; Alzheimer Forschung Initiative; National Institutes of Health; National Ataxia Foundation","keywords":"Spinocerebellar ataxia; Pons; Spinal cord; Ataxia; Cerebellum; Medulla oblongata; Medicine; Machado–Joseph disease; Pathology; Neuroscience; Anatomy; Psychology; Central nervous system","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00005893776,0.0001596933,0.0001383898,0.00006733679,0.00008765973,0.00004970791,0.0001402808,0.00003129718,0.0002675274],"category_scores_gemma":[0.0002786102,0.0001754274,0.00003841216,0.0003593956,0.0001486398,0.00007333597,0.0001365764,0.00009595937,0.00005594619],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003253757,"about_ca_system_score_gemma":0.00009146322,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003993355,"about_ca_topic_score_gemma":0.000234347,"domain_scores_codex":[0.9985283,0.000134443,0.0001851163,0.0005728911,0.0002858284,0.0002934024],"domain_scores_gemma":[0.9995351,0.00003992367,0.00004762296,0.000248825,0.0000328384,0.00009566487],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0004919012,0.0007765555,0.3750312,0.0001015975,0.00001402595,0.0002429101,0.0001760724,0.0004021565,0.5612591,0.005830634,0.04173337,0.0139405],"study_design_scores_gemma":[0.002323033,0.001095313,0.6665037,0.00006348567,0.00001853639,0.000005053747,0.0003433765,0.0008440373,0.2576945,0.02837651,0.04198984,0.0007426845],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9897976,0.0004992367,0.00008691401,0.008590795,0.0001677926,0.0001930958,0.00001481127,0.00002341041,0.0006263656],"genre_scores_gemma":[0.9754459,0.0003619769,0.00009812713,0.02167657,0.00002530559,0.00001650292,0.00001009216,0.00002016965,0.002345417],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.3035646,"threshold_uncertainty_score":0.7153723,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02943543554197124,"score_gpt":0.2803200973060136,"score_spread":0.2508846617640423,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}