{"id":"W3157327845","doi":"10.1002/mds.28610","title":"Regional Brain and Spinal Cord Volume Loss in Spinocerebellar Ataxia Type 3","year":2021,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":59,"is_retracted":false,"has_abstract":true,"ca_institutions":"Western University","funders":"IXICO; Bundesministerium für Gesundheit; National Institute of Neurological Disorders and Stroke; Bundesministerium für Bildung und Forschung; Radboud Universiteit; ZonMw; Agence Nationale de la Recherche; National Institute of Biomedical Imaging and Bioengineering; E-Rare; EU Joint Programme – Neurodegenerative Disease Research; Medical Research Council; AveXis; Biogen; European Commission; Pfizer; Deutsche Forschungsgemeinschaft; Robert Bosch Stiftung; Hersenstichting; Eberhard Karls Universität Tübingen; Alzheimer Forschung Initiative; National Institutes of Health; National Ataxia Foundation","keywords":"Spinocerebellar ataxia; Pons; Spinal cord; Ataxia; Cerebellum; Medulla oblongata; Medicine; Machado–Joseph disease; Pathology; Neuroscience; Anatomy; Psychology; Central nervous system","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000252816,0.0002981017,0.0002247213,0.0006256075,0.0001633449,0.0002275004,0.0001769244,0.0002571312,0.0008367079],"category_scores_gemma":[0.0006175057,0.00009653253,0.0002335622,0.0003922476,0.0003071068,0.0001239195,0.0001898397,0.0001931866,0.00009863228],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003772094,"about_ca_system_score_gemma":0.0002299321,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01109213,"about_ca_topic_score_gemma":0.012995,"domain_scores_codex":[0.999915,0.00001583026,0.000006632442,0.00003239249,0.00002048867,0.000009634717],"domain_scores_gemma":[0.9997134,0.00004776969,0.000162832,0.00002165953,0.00002361721,0.00003079317],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00070763,0.00004610592,0.9556104,0.0000326585,0.0002209621,0.0004665481,0.0002188471,0.001608728,0.03169834,0.00005631453,0.0001329851,0.00920056],"study_design_scores_gemma":[0.000002035912,0.00006819933,0.9983459,0.000001986402,0.00001813053,0.0003031678,0.0000287244,0.0006079952,0.0005490381,0.00003430923,0.00003889296,0.000001658721],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9995322,0.00009737258,0.0002027554,0.000004928467,5.365647e-7,0.000002278078,0.000083303,0.00000733708,0.00006926766],"genre_scores_gemma":[0.9995092,0.00003761099,0.0002398907,0.000003068738,8.167321e-7,0.000003067974,0.0001501835,0.000002976635,0.00005312353],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01109213,"threshold_uncertainty_score":0.02205515,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02943543554197124,"score_gpt":0.2803200973060136,"score_spread":0.2508846617640423,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}