{"id":"W3159236302","doi":"10.1590/s0004-2803.202100000-15","title":"LONG TERM MANAGEMENT OF GLYCOGEN STORAGE DISEASE TYPE 1B: A BRAZILIAN TERTIARY CENTER EXPERIENCE","year":2021,"lang":"en","type":"article","venue":"Arquivos de Gastroenterologia","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Filgrastim; Glycogen storage disease; Neutropenia; Glycogen storage disease type I; Inflammatory bowel disease; Pediatrics; Disease; Retrospective cohort study; Demographics; Surgery; Internal medicine; Chemotherapy","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00007924114,0.0002528847,0.0003392313,0.00007888754,0.00006108401,0.0000245322,0.0002178931,0.00006095048,0.0004983335],"category_scores_gemma":[0.00003478874,0.0002342091,0.0002442909,0.0001818447,0.0001382266,0.0001021882,0.0002700803,0.0001486524,0.00004006466],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001006358,"about_ca_system_score_gemma":0.00007395642,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000009158926,"about_ca_topic_score_gemma":0.000006942224,"domain_scores_codex":[0.9981144,0.00007738897,0.0003676304,0.0005067679,0.0003221339,0.0006116906],"domain_scores_gemma":[0.9984679,0.00001197039,0.0001180585,0.0007283684,0.0001452014,0.0005284634],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.002024731,0.001113845,0.9548542,0.000421659,0.0003111746,0.03227227,0.0002273525,0.000009091214,0.005958798,0.00002752062,0.0007496663,0.002029697],"study_design_scores_gemma":[0.002743493,0.0003541338,0.9930604,0.0003259151,0.0003542106,0.0007572794,0.0002712953,0.00006861401,0.001437855,0.00001295913,0.0004791789,0.0001347367],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9968982,0.0008530826,0.0008079525,0.0003649032,0.0002658601,0.0003606867,0.00006127394,0.00007648071,0.0003115079],"genre_scores_gemma":[0.9950609,0.0001776826,0.001196564,0.002468889,0.00008051029,0.0000504071,0.0001764806,0.00003485034,0.0007537109],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.03820613,"threshold_uncertainty_score":0.9550769,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01259593709885598,"score_gpt":0.2753229990778499,"score_spread":0.2627270619789939,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}