{"id":"W3159236302","doi":"10.1590/s0004-2803.202100000-15","title":"LONG TERM MANAGEMENT OF GLYCOGEN STORAGE DISEASE TYPE 1B: A BRAZILIAN TERTIARY CENTER EXPERIENCE","year":2021,"lang":"en","type":"article","venue":"Arquivos de Gastroenterologia","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Filgrastim; Glycogen storage disease; Neutropenia; Glycogen storage disease type I; Inflammatory bowel disease; Pediatrics; Disease; Retrospective cohort study; Demographics; Surgery; Internal medicine; Chemotherapy","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003370815,0.0003821341,0.0002450578,0.0004379761,0.001308808,0.0005350423,0.000474469,0.0007623665,0.001937035],"category_scores_gemma":[0.001425485,0.0002177042,0.000264228,0.0007137291,0.0005089488,0.0003467062,0.001004362,0.0004940618,0.0002431308],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001021029,"about_ca_system_score_gemma":0.001170081,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006509408,"about_ca_topic_score_gemma":0.01075378,"domain_scores_codex":[0.9997281,0.00005765315,0.00003102209,0.00003915506,0.00003572253,0.0001082472],"domain_scores_gemma":[0.9990581,0.0001010786,0.0003579815,0.0000374251,0.00007041608,0.0003750745],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001088276,0.0004376334,0.8236939,0.0002153623,0.00004088701,0.1432432,0.00405454,0.0001878997,0.002587326,0.0003720265,0.002137861,0.02292055],"study_design_scores_gemma":[0.00006569934,0.001256038,0.5950927,0.0005693398,0.00007224447,0.3823709,0.01059568,0.0004586024,0.0007622621,0.0004467374,0.008260612,0.00004914557],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9941666,0.002271337,0.0002192702,0.0006020549,0.00002843438,0.00003141087,0.00008053608,0.00000874263,0.002591496],"genre_scores_gemma":[0.9974481,0.001438274,0.0002072514,0.0004018477,0.00003723787,0.00001701947,0.0001148193,0.000005984613,0.0003295003],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.006509408,"threshold_uncertainty_score":0.01294309,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01259593709885598,"score_gpt":0.2753229990778499,"score_spread":0.2627270619789939,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}