{"id":"W3169628450","doi":"10.3390/cells10061532","title":"Fabry Cardiomyopathy: Current Practice and Future Directions","year":2021,"lang":"en","type":"review","venue":"Cells","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":24,"is_retracted":false,"has_abstract":true,"ca_institutions":"Vancouver General Hospital; University of British Columbia","funders":"","keywords":"Fabry disease; Enzyme replacement therapy; Medicine; Cardiomyopathy; Magnetic resonance imaging; Disease; Cardiology; Heart failure; Internal medicine; Hypertrophic cardiomyopathy; Intensive care medicine; Radiology; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001612577,0.0008152479,0.001643324,0.003461505,0.000394219,0.001919072,0.001279351,0.002182755,0.007550256],"category_scores_gemma":[0.002502382,0.0003048617,0.0006820035,0.002770507,0.0008686797,0.00314069,0.001099473,0.002401913,0.003030879],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001103129,"about_ca_system_score_gemma":0.002306787,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001206477,"about_ca_topic_score_gemma":0.002235901,"domain_scores_codex":[0.9996234,0.00008003516,0.00007389192,0.00007049827,0.0001155361,0.00003660697],"domain_scores_gemma":[0.9980652,0.001002118,0.000192323,0.00004776627,0.0005076496,0.0001849485],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0000995701,0.00006452205,0.0002203633,0.01760511,0.00005702414,0.000310281,0.00008562657,0.0002791435,0.0003999319,0.005679015,0.06702022,0.9081791],"study_design_scores_gemma":[0.00002467437,0.00005569063,0.0005461418,0.009996442,0.00009470422,0.001391722,0.0001282107,0.00009970796,0.00008434583,0.004581052,0.9829743,0.00002300878],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0000422804,0.9972203,0.00007175162,0.001565185,0.0003979859,0.000002386906,0.00001112385,0.000009205164,0.0006798174],"genre_scores_gemma":[0.0003675323,0.9977564,0.0001585219,0.0007480043,0.0006242355,0.000005081672,0.00002108839,0.000001750477,0.0003173095],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.007550256,"threshold_uncertainty_score":0.02525818,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04720978919698247,"score_gpt":0.3900966857887531,"score_spread":0.3428868965917706,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}