{"id":"W3177560676","doi":"","title":"Natural history study of visual function in patients with BBS1- and BBS10-related retinal degeneration.","year":2021,"lang":"en","type":"article","venue":"Investigative Ophthalmology & Visual Science","topic":"Retinal Development and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Retinal degeneration; Retinal; Ophthalmology; Degeneration (medical); Macular degeneration; Medicine; Optometry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002709575,0.0001425282,0.0001577701,0.0001049755,0.0001017943,0.00001164952,0.0001102012,0.00007609353,0.0000253248],"category_scores_gemma":[0.0002280638,0.0001252465,0.00001565754,0.0004078748,0.001225723,0.00002606483,0.0001341206,0.0001180082,0.000001400387],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00005653045,"about_ca_system_score_gemma":0.0004330147,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00004018457,"about_ca_topic_score_gemma":0.00003669731,"domain_scores_codex":[0.9986048,0.0001623227,0.0002400225,0.0005165821,0.000263167,0.0002130642],"domain_scores_gemma":[0.9993485,0.00001533786,0.0001292437,0.0001087218,0.0003156054,0.00008261572],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001432736,0.0002949855,0.6123422,0.000004210602,0.00001328876,0.00001215289,0.0003938617,0.00001417632,0.3866706,0.00001594323,0.00001637939,0.00007882461],"study_design_scores_gemma":[0.001198834,0.002672786,0.9186406,0.00001374539,0.00001149239,0.00001662487,0.0006331201,0.00004992956,0.07650707,0.00008219085,0.0000173304,0.0001563294],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9989674,0.0002752173,0.000001463524,0.0000237327,0.0001763413,0.0002035056,7.550283e-7,0.000004095156,0.000347466],"genre_scores_gemma":[0.9994232,0.000002898959,0.000212966,0.000059954,0.00001106659,0.00001390563,0.00004299625,0.000007629892,0.0002253766],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.3101636,"threshold_uncertainty_score":0.5107404,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01218795956884002,"score_gpt":0.263072765936115,"score_spread":0.250884806367275,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}