{"id":"W3183513593","doi":"10.1007/s12311-021-01305-z","title":"Cognitive Decline Is Closely Associated with Ataxia Severity in Spinocerebellar Ataxia Type 2: a Validation Study of the Schmahmann Syndrome Scale","year":2021,"lang":"en","type":"article","venue":"The Cerebellum","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":47,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"","keywords":"Montreal Cognitive Assessment; Spinocerebellar ataxia; Psychology; Cronbach's alpha; Cognition; Cognitive test; Discriminant validity; Cerebellar ataxia; Ataxia; Physical therapy; Psychometrics; Internal consistency; Audiology; Physical medicine and rehabilitation; Clinical psychology; Psychiatry; Medicine; Cognitive impairment","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000291574,0.0002440584,0.0003241246,0.00005521333,0.0002699303,0.00005905715,0.0005479683,0.00006131411,0.0001797459],"category_scores_gemma":[0.001235093,0.0001586173,0.00007055458,0.0015288,0.0002658634,0.0001085429,0.000464258,0.0002929957,0.00005014736],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00005271676,"about_ca_system_score_gemma":0.0002408556,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00009836295,"about_ca_topic_score_gemma":0.0008426717,"domain_scores_codex":[0.9966438,0.001327935,0.0003696724,0.0006233952,0.0007077614,0.00032745],"domain_scores_gemma":[0.9982546,0.0003726745,0.0002857413,0.0006919338,0.0003268958,0.00006816474],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004301016,0.004222039,0.8151627,0.00005691885,0.000125028,0.0001748085,0.005043228,0.0007822542,0.1732724,0.00003627645,0.0004233313,0.0002708972],"study_design_scores_gemma":[0.001087254,0.0002887051,0.5036138,0.00007741644,0.00009287696,0.00002386085,0.0005939635,0.0001695064,0.4937377,0.0001412565,0.00002202046,0.0001517107],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9978977,0.00006979276,0.00001017307,0.0004193737,0.0001727375,0.0009597656,0.0001445786,0.00003025018,0.0002956091],"genre_scores_gemma":[0.9977945,0.00001898671,0.000009191298,0.0008899496,0.0000181468,0.0000259614,0.00001494323,0.00003421278,0.001194116],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.3204652,"threshold_uncertainty_score":0.6468225,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03379304295944265,"score_gpt":0.2744302285572844,"score_spread":0.2406371855978418,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}