{"id":"W3186573778","doi":"10.1016/j.pediatrneurol.2021.07.011","title":"Updated International Tuberous Sclerosis Complex Diagnostic Criteria and Surveillance and Management Recommendations","year":2021,"lang":"en","type":"article","venue":"Pediatric Neurology","topic":"Tuberous Sclerosis Complex Research","field":"Medicine","cited_by":705,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"Tuberous Sclerosis Association; Upsher-Smith; H. Lundbeck A/S; LivaNova; Depomed; Amneal Pharmaceuticals; Mallinckrodt Pharmaceuticals; Greenwich Biosciences; Tuberous Sclerosis Alliance","keywords":"Tuberous sclerosis; TSC1; Medicine; Presentation (obstetrics); Genetic testing; Pediatrics; Pathology; Surgery; Internal medicine","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.01054769,0.0008964211,0.001574016,0.005484713,0.00113011,0.002266416,0.002357457,0.004737958,0.004542531],"category_scores_gemma":[0.03959544,0.0006871838,0.002531823,0.003232739,0.0006092344,0.002183596,0.001785963,0.008054472,0.002152105],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.004139129,"about_ca_system_score_gemma":0.01320347,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.05213149,"about_ca_topic_score_gemma":0.05909758,"domain_scores_codex":[0.9923815,0.001906134,0.002371181,0.0003042139,0.002353381,0.00068348],"domain_scores_gemma":[0.9659249,0.005743155,0.004156705,0.0005135886,0.02112442,0.002537232],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001420833,0.0002765621,0.01449396,0.0008007745,0.0002037791,0.0003018792,0.0002881719,0.001331175,0.0002289464,0.001937646,0.7859699,0.1940251],"study_design_scores_gemma":[0.0006935906,0.0002008084,0.0962579,0.01542698,0.001088019,0.002287733,0.001086202,0.002346107,0.0006977603,0.0067207,0.8729475,0.0002466535],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"methods","genre_scores_codex":[0.01313114,0.1614338,0.01698237,0.6706927,0.03609527,0.001573911,0.02330637,0.001020334,0.07576394],"genre_scores_gemma":[0.1198489,0.2743139,0.1602486,0.2605785,0.03747659,0.005237731,0.0974562,0.0004677923,0.04437171],"genre_candidate":"methods","genre_consensus":null,"teacher_disagreement_score":0.05213149,"threshold_uncertainty_score":0.1036561,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05552967818157058,"score_gpt":0.3193548388332552,"score_spread":0.2638251606516847,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}