{"id":"W3192668141","doi":"10.1183/16000617.0348-2020","title":"Tuberous sclerosis complex for the pulmonologist","year":2021,"lang":"en","type":"article","venue":"European Respiratory Review","topic":"Tuberous Sclerosis Complex Research","field":"Medicine","cited_by":33,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hôpital Charles-Le Moyne; Université de Sherbrooke","funders":"","keywords":"Tuberous sclerosis; Medicine; TSC1; TSC2; Lymphangioleiomyomatosis; Penetrance; Sirolimus; Genetic disorder; Pathology; PI3K/AKT/mTOR pathway; Internal medicine; Disease; Phenotype","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004057904,0.0005663395,0.0005040935,0.0007542123,0.0006005261,0.001186252,0.00053775,0.001661892,0.04574129],"category_scores_gemma":[0.00230732,0.0001479306,0.0003179507,0.0004000654,0.0003429897,0.001113251,0.0008339448,0.002854234,0.02325749],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005156354,"about_ca_system_score_gemma":0.001029212,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0006574441,"about_ca_topic_score_gemma":0.001812474,"domain_scores_codex":[0.9996685,0.00008597288,0.0000357068,0.00005680835,0.00009006153,0.00006284987],"domain_scores_gemma":[0.9990784,0.000160488,0.00007118096,0.00004657107,0.0003321035,0.0003112634],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00002854554,0.00003174914,0.0007386756,0.0003473256,0.00001480025,0.00354875,0.00006548948,0.00002360301,0.0003261851,0.001192019,0.8342942,0.1593886],"study_design_scores_gemma":[0.00001550627,0.00001984739,0.0008207476,0.0005116533,0.00001077472,0.01566235,0.00007891987,0.00002354128,0.0000457421,0.0004884521,0.9823163,0.000006155657],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00331987,0.5434561,0.002237264,0.1646122,0.1143868,0.000129546,0.0004362873,0.0005745547,0.1708474],"genre_scores_gemma":[0.0532249,0.3871778,0.003141508,0.1153101,0.1400443,0.0001363016,0.001047506,0.0001629751,0.2997546],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.04574129,"threshold_uncertainty_score":0.1530198,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.373440678423274,"score_gpt":0.3848530262708441,"score_spread":0.01141234784757011,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}