{"id":"W3195942024","doi":"10.3390/children8090721","title":"Clinical Course, Myopathology and Challenge of Therapeutic Intervention in Pediatric Patients with Autoimmune-Mediated Necrotizing Myopathy","year":2021,"lang":"en","type":"article","venue":"Children","topic":"Inflammatory Myopathies and Dermatomyositis","field":"Medicine","cited_by":15,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario; University of Ottawa","funders":"","keywords":"Juvenile dermatomyositis; Muscle biopsy; Medicine; Inflammatory myopathy; Muscular dystrophy; Weakness; Limb-girdle muscular dystrophy; Muscle weakness; Myopathy; Pathology; Dystrophin; Biopsy; Immunology; Internal medicine; Disease; Surgery; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002446803,0.0005119999,0.0003611902,0.0003965159,0.0004255459,0.0003301099,0.0002192172,0.0007620346,0.000876167],"category_scores_gemma":[0.001050205,0.000150048,0.0002058821,0.0003419392,0.0003540978,0.0004164576,0.000306225,0.0006096119,0.000190977],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004892705,"about_ca_system_score_gemma":0.0003969415,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009024832,"about_ca_topic_score_gemma":0.001087354,"domain_scores_codex":[0.9998152,0.00003371874,0.00002555951,0.00004057997,0.00003266167,0.00005237344],"domain_scores_gemma":[0.9995877,0.00007057554,0.0001491958,0.00001301657,0.00004146786,0.0001380823],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002821047,0.00008174986,0.811708,0.0001195958,0.00002457333,0.167716,0.000505672,0.000340211,0.004905539,0.0001784253,0.0007568573,0.01338118],"study_design_scores_gemma":[0.00002822145,0.00056677,0.5584258,0.0001013689,0.00004238509,0.4371322,0.0006206872,0.0004393133,0.0009287535,0.0001768763,0.001523867,0.00001377844],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9942505,0.002823335,0.000528108,0.0003781493,0.00002157225,0.00003167588,0.0001322396,0.00002482956,0.001809658],"genre_scores_gemma":[0.997996,0.0009779306,0.0005145286,0.0001220825,0.00006881874,0.00001748425,0.0001543631,0.000004712928,0.0001441426],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0009024832,"threshold_uncertainty_score":0.003549874,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009040839008687936,"score_gpt":0.2684212298035643,"score_spread":0.2593803907948763,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}