{"id":"W319702943","doi":"10.1023/a:1024048118294","title":"The relationship of plasma glutamine to ammonium and of glycine to acid–base balance in propionic acidaemia","year":2003,"lang":"en","type":"article","venue":"Journal of Inherited Metabolic Disease","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":26,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario","funders":"","keywords":"Glutamine; Hyperammonemia; Urea cycle; Internal medicine; Phenylbutyrate; Chemistry; Endocrinology; Glycine; Sodium bicarbonate; Bicarbonate; Ammonium; Acid–base homeostasis; Biochemistry; Amino acid; Medicine; Arginine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005072355,0.0001330376,0.0002869607,0.0001384134,0.0000382099,0.00001303172,0.0001883955,0.00005535824,0.000007472318],"category_scores_gemma":[0.001782041,0.0000958434,0.00008710398,0.0003893983,0.00007539699,0.000008139838,0.00004734443,0.00008140265,9.805786e-7],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000003172321,"about_ca_system_score_gemma":0.000199487,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000006135482,"about_ca_topic_score_gemma":0.00002552716,"domain_scores_codex":[0.9987054,0.000152367,0.0005780298,0.0001584112,0.0002153473,0.0001904856],"domain_scores_gemma":[0.9989134,0.00003838481,0.0002691467,0.0002903593,0.0002007585,0.000287956],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.00359605,0.0004394896,0.220647,0.0001398605,0.0001395624,0.00001563766,0.0003457248,0.001154671,0.7535249,0.002521831,0.001033599,0.0164417],"study_design_scores_gemma":[0.002435656,0.0002966902,0.793479,0.0001180539,0.0001188297,0.00001595773,0.0003140707,0.00002629807,0.1535121,0.0003351443,0.04914946,0.0001987025],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9833277,0.0153883,0.0003268977,0.000460322,0.0001279329,0.000240495,0.00002548744,0.000001155906,0.000101727],"genre_scores_gemma":[0.9965238,0.001161652,0.001897396,0.0001707512,0.00005508131,0.00001114609,0.000003878763,0.00001377065,0.0001625346],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6000128,"threshold_uncertainty_score":0.390838,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01000711527123785,"score_gpt":0.2514420541705438,"score_spread":0.2414349388993059,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}