{"id":"W3210285596","doi":"10.1007/s10875-021-01162-9","title":"Late-Onset Combined Immunodeficiency with Refractory CMV Disease due to ICOSL Deficiency","year":2021,"lang":"en","type":"letter","venue":"Journal of Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":5,"is_retracted":false,"has_abstract":false,"ca_institutions":"McGill University Health Centre","funders":"Fonds de Recherche du Québec - Santé","keywords":"Immunodeficiency; Medical microbiology; Medicine; Primary immunodeficiency; Refractory (planetary science); Immunology; Severe combined immunodeficiency; Human immunodeficiency virus (HIV); Virology; Biology; Immune system","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","research_integrity","insufficient_payload"],"consensus_categories":["research_integrity","insufficient_payload"],"category_scores_codex":[0.002697226,0.001201012,0.004029122,0.0009514966,0.0005943244,0.0001191752,0.002919992,0.003212853,0.001639313],"category_scores_gemma":[0.003372038,0.0009375735,0.00175869,0.0009670141,0.002420109,0.0003724554,0.000648735,0.0120052,0.001144392],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001812346,"about_ca_system_score_gemma":0.003086828,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00007146163,"about_ca_topic_score_gemma":0.000003658426,"domain_scores_codex":[0.9882661,0.002918547,0.005258818,0.001250199,0.0004591605,0.001847142],"domain_scores_gemma":[0.989675,0.002604717,0.003947442,0.002117311,0.001570464,0.00008508953],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0205397,0.0103627,0.003657636,0.0005634864,0.009010093,0.02522586,0.001862071,0.0002426441,0.0117088,0.000283027,0.8551272,0.06141683],"study_design_scores_gemma":[0.00676091,0.006627578,0.02814901,0.000994712,0.001224738,0.002464717,0.0005976624,0.000002339393,0.0003311956,0.0003640019,0.9510369,0.001446248],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.568501,0.1875439,0.0005430242,0.2222603,0.01829863,0.0009500181,0.00022373,0.0001581138,0.001521303],"genre_scores_gemma":[0.6768087,0.005161785,0.0002761729,0.3013403,0.0005287429,0.0000707714,0.001199019,0.0003493167,0.0142652],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1823821,"threshold_uncertainty_score":0.9996333,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02749125358685371,"score_gpt":0.3029825944414867,"score_spread":0.2754913408546329,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}