{"id":"W3210285596","doi":"10.1007/s10875-021-01162-9","title":"Late-Onset Combined Immunodeficiency with Refractory CMV Disease due to ICOSL Deficiency","year":2021,"lang":"en","type":"letter","venue":"Journal of Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":5,"is_retracted":false,"has_abstract":false,"ca_institutions":"McGill University Health Centre","funders":"Fonds de Recherche du Québec - Santé","keywords":"Immunodeficiency; Medical microbiology; Medicine; Primary immunodeficiency; Refractory (planetary science); Immunology; Severe combined immunodeficiency; Human immunodeficiency virus (HIV); Virology; Biology; Immune system","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0009810149,0.002249662,0.001541329,0.00146032,0.002074648,0.001440383,0.001635669,0.01252341,0.002764986],"category_scores_gemma":[0.00658355,0.0008046742,0.001323104,0.0008905237,0.001641145,0.001606901,0.0007056709,0.007015415,0.001097056],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.002141451,"about_ca_system_score_gemma":0.001293499,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002963222,"about_ca_topic_score_gemma":0.003290584,"domain_scores_codex":[0.9990946,0.0002247924,0.00009408978,0.0001386195,0.0001717336,0.000276151],"domain_scores_gemma":[0.9979565,0.0009676759,0.0001825532,0.0001289532,0.0001422452,0.0006219277],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0002207364,0.00006221662,0.004536647,0.00005035866,0.00001255875,0.9879308,0.00007608276,0.00009762988,0.0006014585,0.0006075581,0.00448433,0.001319725],"study_design_scores_gemma":[0.00025698,0.0003541832,0.009738956,0.0001093746,0.00005057317,0.977142,0.0002299554,0.001747582,0.0006349672,0.001780338,0.007922999,0.00003196339],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.5871578,0.01407069,0.006222534,0.2029889,0.02539689,0.0006230072,0.0009433361,0.000694386,0.1619025],"genre_scores_gemma":[0.9248584,0.00241333,0.001602478,0.03164091,0.02694835,0.00008239724,0.0002316967,0.00008309611,0.01213934],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01252341,"threshold_uncertainty_score":0.01553732,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02749125358685371,"score_gpt":0.3029825944414867,"score_spread":0.2754913408546329,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}