{"id":"W3217787228","doi":"10.3390/ijms222312617","title":"Natural History of a Mouse Model Overexpressing the Dp71 Dystrophin Isoform","year":2021,"lang":"en","type":"article","venue":"International Journal of Molecular Sciences","topic":"Muscle Physiology and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"Muscular Dystrophy Canada; University of Alberta","funders":"Canadian Institutes of Health Research; Alberta Innovates; Leids Universitair Medisch Centrum; Universiteit Leiden; Canada Foundation for Innovation; University of Alberta; Alberta Innovates - Health Solutions; Canada Research Chairs; Women and Children's Health Research Institute; Children's Health Research Institute","keywords":"Dystrophin; Duchenne muscular dystrophy; Skeletal muscle; Gene isoform; Biology; Muscular dystrophy; Cardiac muscle; ITGA7; Transgene; Myocyte; Cell biology; Exon; Utrophin; Molecular biology; Internal medicine; Gene; Endocrinology; Genetics; Medicine","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002081741,0.0006273949,0.0003074387,0.001123304,0.0005594029,0.0003787983,0.0003028365,0.0009051748,0.004201787],"category_scores_gemma":[0.0003301002,0.0002031289,0.0003239148,0.0003087823,0.000495262,0.000457096,0.000415345,0.0009116108,0.001257354],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003225825,"about_ca_system_score_gemma":0.0002100903,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005314393,"about_ca_topic_score_gemma":0.0005618355,"domain_scores_codex":[0.9997887,0.00002985072,0.00001363081,0.00008424975,0.00004560442,0.00003793807],"domain_scores_gemma":[0.999557,0.00006397907,0.0001123898,0.00004743335,0.00004404142,0.0001751108],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.002845825,0.003073862,0.04136822,0.0002489407,0.00009293065,0.04002462,0.0003795756,0.0002843016,0.865721,0.004327572,0.007068763,0.03456439],"study_design_scores_gemma":[0.0006158407,0.01262758,0.2717065,0.0003613711,0.0005315298,0.3610785,0.000677399,0.003941909,0.2449913,0.004303271,0.0988717,0.0002930161],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9831653,0.002346168,0.003124252,0.0008701207,0.0001043554,0.0001194033,0.001581224,0.00033282,0.008356392],"genre_scores_gemma":[0.9728339,0.00208552,0.00174531,0.0007209929,0.00006666965,0.000206944,0.002663929,0.0001274042,0.01954938],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004201787,"threshold_uncertainty_score":0.01405644,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01292916465083723,"score_gpt":0.2651627163987099,"score_spread":0.2522335517478727,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}