{"id":"W32573447","doi":"10.1016/j.eplepsyres.2006.07.009","title":"Protein therapy for Unverricht–Lundborg disease using cystatin B transduction by TAT-PTD","year":2006,"lang":"en","type":"article","venue":"Epilepsy Research","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":7,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"Centre Scientifique et Technique du Bâtiment; Canadian Institutes of Health Research; Hospital for Sick Children; Canada Research Chairs","keywords":"Transduction (biophysics); Cystatin C; Epilepsy; Medicine; Progressive myoclonus epilepsy; Neuroscience; Disease; Internal medicine; Biology; Biochemistry","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007613492,0.000193905,0.0002759556,0.0002216116,0.0003626058,0.00006607301,0.0001360357,0.00009125862,0.0004651735],"category_scores_gemma":[0.0001493124,0.0001690474,0.0002074874,0.0005088151,0.0001783872,0.000125898,0.00001978799,0.0002953994,0.00004567123],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001883997,"about_ca_system_score_gemma":0.0004261796,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0010584,"about_ca_topic_score_gemma":0.00001308733,"domain_scores_codex":[0.9974087,0.000204608,0.0003190437,0.000501763,0.0008364298,0.0007293809],"domain_scores_gemma":[0.9985393,0.00009869315,0.00005548996,0.0003964494,0.0004811031,0.000429004],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"not_applicable","study_design_scores_codex":[0.01309769,0.002898177,0.008631974,0.000835111,0.0001874281,0.001187877,0.0002831362,0.00008068954,0.8020001,0.001624409,0.1401829,0.02899051],"study_design_scores_gemma":[0.02901238,0.005190332,0.03338126,0.0009513518,0.0004284832,0.000229119,0.001241224,0.01597056,0.1183803,0.0106555,0.7828758,0.001683699],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9841523,0.005370651,0.004091686,0.002025733,0.0001188097,0.003419043,0.0002866372,0.00008327161,0.0004518905],"genre_scores_gemma":[0.9901014,0.0001073961,0.001723597,0.0001515545,0.0006637905,0.00060781,0.0003959521,0.0000782972,0.006170191],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6836198,"threshold_uncertainty_score":0.6893554,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.07000446861703974,"score_gpt":0.3867258222625597,"score_spread":0.31672135364552,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}