{"id":"W4205105426","doi":"10.1007/978-3-030-23810-0_100","title":"Autosomal Recessive Cerebellar Ataxias","year":2021,"lang":"en","type":"book-chapter","venue":"","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":1,"is_retracted":false,"has_abstract":false,"ca_institutions":"Centre hospitalier universitaire de Québec; Université Laval; Université de Montréal; Hôpital de l'Enfant-Jésus; McGill University; Montreal Neurological Institute and Hospital","funders":"","keywords":"Ataxia; Spinocerebellar ataxia; Cerebellar ataxia; Genetics; Medicine; Biology; Neuroscience","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001363804,0.0008463931,0.0004396277,0.0008347597,0.0003196375,0.0006783259,0.0005168062,0.0008644484,0.02907294],"category_scores_gemma":[0.0002273857,0.0001903598,0.0002591859,0.0004709133,0.0003855141,0.0007309208,0.000806746,0.001003288,0.01603018],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000444267,"about_ca_system_score_gemma":0.0003019929,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000946075,"about_ca_topic_score_gemma":0.003547093,"domain_scores_codex":[0.999931,0.000009394908,0.000004110411,0.00001133223,0.00003415783,0.00001000491],"domain_scores_gemma":[0.9999387,0.00002668773,0.000004881811,0.000004594872,0.00001251448,0.00001256087],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00004477508,0.00005506174,0.0001738977,0.000307711,0.00001237626,0.001728528,0.0001425138,0.000627324,0.002945433,0.04919824,0.5182146,0.4265495],"study_design_scores_gemma":[0.000004637878,0.00001862606,0.0002874648,0.0001145537,0.000004397953,0.003206686,0.00001779485,0.0001045898,0.0003007969,0.006616213,0.9893194,0.000004794986],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"other","genre_gemma":"review","genre_scores_codex":[0.002391435,0.1033589,0.008908203,0.004004593,0.005508729,0.00004649296,0.0003060496,0.0005874226,0.8748881],"genre_scores_gemma":[0.006527963,0.04312217,0.002728091,0.001705404,0.001442574,0.00003612822,0.0002472606,0.0001059689,0.9440845],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.02907294,"threshold_uncertainty_score":0.09725869,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04396442340933768,"score_gpt":0.2623534677131943,"score_spread":0.2183890443038567,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}