{"id":"W4205810635","doi":"10.1017/cjn.2021.382","title":"P.104 Children with Trisomy 21 and Lennox-Gastaut Syndrome with predominant myoclonic seizures","year":2021,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Vancouver Biotech (Canada)","funders":"","keywords":"Lennox–Gastaut syndrome; Pediatrics; Epilepsy; Myoclonic epilepsy; Trisomy; Medicine; Seizure types; Down syndrome; Intellectual disability; Medical record; Electroencephalography; Psychology; Audiology; Psychiatry; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001899614,0.0003796608,0.0002194174,0.00113754,0.0003954917,0.0003240977,0.0002440892,0.000359307,0.01217921],"category_scores_gemma":[0.001021901,0.0002304316,0.0001673367,0.001209205,0.0003449692,0.000351014,0.0003223102,0.0003514232,0.002122006],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000229097,"about_ca_system_score_gemma":0.0003581902,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001691219,"about_ca_topic_score_gemma":0.001210542,"domain_scores_codex":[0.9998249,0.00003069179,0.00002500771,0.00003974628,0.00004558189,0.00003407225],"domain_scores_gemma":[0.9996132,0.0001300916,0.0001477833,0.00002061147,0.00003172148,0.00005665448],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0001312909,0.00008342007,0.9426295,0.00009953387,0.00003245243,0.03817328,0.0002581483,0.00008675945,0.0008182009,0.0001724197,0.004641727,0.01287336],"study_design_scores_gemma":[0.00005078077,0.000351998,0.7151949,0.0000959976,0.00004493922,0.2721859,0.0004420655,0.0002923408,0.0006864782,0.0002636194,0.01038043,0.00001064688],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9775078,0.002160823,0.0006864222,0.0004693488,0.0001160997,0.0001938119,0.003004623,0.00009377846,0.01576741],"genre_scores_gemma":[0.9913886,0.001546739,0.0007255553,0.000383993,0.0002683123,0.0002176271,0.002082374,0.00002319886,0.003363608],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01217921,"threshold_uncertainty_score":0.04074347,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009020018439294064,"score_gpt":0.2174657197932753,"score_spread":0.2084457013539812,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}