{"id":"W4206522761","doi":"10.3410/f.5917956.14076054","title":"Faculty Opinions recommendation of ALS-associated fused in sarcoma (FUS) mutations disrupt Transportin-mediated nuclear import.","year":2011,"lang":"en","type":"dataset","venue":"Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Neurological Institute and Hospital","funders":"Canadian Institutes of Health Research; Hans und Ilse Breuer-Stiftung; Bundesministerium für Bildung und Forschung","keywords":"Nuclear transport; Frontotemporal lobar degeneration; NLS; Amyotrophic lateral sclerosis; Nuclear localization sequence; Stress granule; Pathogenesis; Nuclear export signal; Cytoplasm; Biology; Neurodegeneration; Nuclear lamina; Cell biology; Cell nucleus; Pathology; Medicine; Cancer research; Nuclear protein; Genetics; Frontotemporal dementia; Disease; Gene; Dementia","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001336377,0.001318706,0.001167365,0.008398447,0.0005585111,0.001766184,0.001572896,0.00125104,0.04397845],"category_scores_gemma":[0.01095568,0.0003134628,0.0009494165,0.01085825,0.0002571912,0.0009031743,0.0009426546,0.0009768999,0.03432154],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001289763,"about_ca_system_score_gemma":0.003546999,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0149139,"about_ca_topic_score_gemma":0.03365041,"domain_scores_codex":[0.9983262,0.0002706758,0.0003480986,0.0003843383,0.0005286007,0.0001420032],"domain_scores_gemma":[0.9933105,0.00189494,0.001534178,0.0007512016,0.001878632,0.0006306802],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0003047741,0.00005355841,0.01138384,0.00456688,0.000301393,0.0001595748,0.000075367,0.0006870939,0.0009890662,0.0006565466,0.9496441,0.03117782],"study_design_scores_gemma":[0.0001544925,0.00003378001,0.02396768,0.0004239972,0.00016065,0.0001799591,0.00007155076,0.0008215917,0.001269308,0.0003950762,0.9724884,0.00003360906],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"dataset","genre_gemma":"dataset","genre_scores_codex":[0.001312235,0.0004766529,0.0001464305,0.0002104288,0.00004728752,0.00003755273,0.9950786,0.0003140829,0.002376814],"genre_scores_gemma":[0.002175467,0.0003257128,0.0005409492,0.00005367723,0.00002029982,0.00006328192,0.9954829,0.00004895531,0.001288778],"genre_candidate":"dataset","genre_consensus":"dataset","teacher_disagreement_score":0.04397845,"threshold_uncertainty_score":0.1471226,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04936572010742353,"score_gpt":0.3649377535735075,"score_spread":0.315572033466084,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}