{"id":"W4206661690","doi":"10.1186/s13223-021-00641-3","title":"Hereditary angioedema due to C1 inhibitor deficiency: real-world experience from the Icatibant Outcome Survey in Spain","year":2021,"lang":"en","type":"article","venue":"Allergy Asthma and Clinical Immunology","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"European Academy of Allergy and Clinical Immunology","keywords":"Icatibant; Hereditary angioedema; Medicine; Angioedema; Internal medicine; C1-inhibitor; Attack rate; Pediatrics; Gastroenterology; Antagonist; Epidemiology; Immunology; Receptor","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001655993,0.0002826314,0.0004125066,0.0009928198,0.0002181495,0.0007991174,0.0004029052,0.0004362585,0.0006707781],"category_scores_gemma":[0.002044073,0.0001708322,0.0003505343,0.001372007,0.0002953046,0.0003364559,0.0006685912,0.0002868771,0.0001838059],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0009789892,"about_ca_system_score_gemma":0.0006869585,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.02124201,"about_ca_topic_score_gemma":0.01697918,"domain_scores_codex":[0.9992155,0.0002698911,0.00009906038,0.0001261112,0.0001421399,0.0001472312],"domain_scores_gemma":[0.9974728,0.0004649246,0.001158862,0.0001510216,0.0004396529,0.0003126938],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001205272,0.00005206345,0.9968381,0.00002149404,0.00003374793,0.0002949818,0.0002365616,0.00006577527,0.00007744222,0.000008726569,0.0002976581,0.001952889],"study_design_scores_gemma":[0.00001450384,0.00007493496,0.9982344,0.00001540452,0.0000154789,0.0003710942,0.0007402798,0.00008665748,0.00003299307,0.000007360457,0.0004028297,0.000004057967],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9982526,0.0003183644,0.00005738558,0.00005174431,0.00000482526,0.00001121572,0.0008770968,0.000003210346,0.0004235175],"genre_scores_gemma":[0.9983852,0.000274687,0.00005747651,0.00005604156,0.000009699421,0.00000953918,0.001076797,0.000002939988,0.0001276695],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02124201,"threshold_uncertainty_score":0.04223675,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05572580944438733,"score_gpt":0.3481916223124576,"score_spread":0.2924658128680703,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}