{"id":"W4207016536","doi":"10.1016/j.autrev.2022.103055","title":"Eculizumab use in catastrophic antiphospholipid syndrome (CAPS): Descriptive analysis from the “CAPS Registry”","year":2022,"lang":"en","type":"review","venue":"Autoimmunity Reviews","topic":"Systemic Lupus Erythematosus Research","field":"Medicine","cited_by":86,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"Department of Obstetrics and Gynecology, University of Wisconsin-Madison; Sorbonne Université; Urmia University of Medical Sciences; Akershus Universitetssykehus; Centre hospitalier universitaire Sainte-Justine; Debreceni Egyetem; McGill University Health Centre; Universidad Nacional Mayor de San Marcos; Gdański Uniwersytet Medyczny; Universidade Federal do Rio de Janeiro; Universidade do Estado do Rio de Janeiro; Shahrekord University of Medical Sciences; Universitetet i Oslo; Mayo Clinic; Tel Aviv University; Tays; Catholic University of Korea; Kagawa University; Fundación Valle del Lili; Cedars-Sinai Medical Center; Department of Haematology, Christian Medical College, Vellore; Universidad de Antioquia; University Hospitals; Central Manchester University Hospitals NHS Foundation Trust","keywords":"Eculizumab; Medicine; Thrombotic microangiopathy; Catastrophic antiphospholipid syndrome; Antiphospholipid syndrome; Atypical hemolytic uremic syndrome; Internal medicine; Pediatrics; Adverse effect; Surgery; Thrombosis; Complement system; Immunology; Antibody; Disease","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001228276,0.0004269952,0.002102959,0.003357153,0.0001350408,0.0007480297,0.0004685051,0.0004048327,0.001757656],"category_scores_gemma":[0.003030479,0.0002630366,0.002286213,0.005875813,0.0001883221,0.0006216443,0.0004757598,0.0006531075,0.0002887344],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004140968,"about_ca_system_score_gemma":0.001497882,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002193308,"about_ca_topic_score_gemma":0.00439153,"domain_scores_codex":[0.9991195,0.0001724146,0.0003410231,0.0001321746,0.0001814112,0.00005360517],"domain_scores_gemma":[0.9977772,0.001160813,0.0007729346,0.00004847192,0.0001832702,0.00005737406],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"observational","study_design_scores_codex":[0.002450058,0.0001356218,0.04876895,0.1744892,0.0158604,0.0004652958,0.0002208075,0.0004745008,0.0009020026,0.0007855115,0.02038756,0.7350602],"study_design_scores_gemma":[0.001932909,0.001461433,0.4167041,0.1771493,0.1011994,0.00738523,0.0008449418,0.0005299475,0.001187486,0.001143906,0.2902028,0.0002585427],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.005068026,0.992988,0.00009333997,0.000114961,0.00005153283,0.00002974594,0.001203265,0.000004836757,0.0004463533],"genre_scores_gemma":[0.01804378,0.9799774,0.0002208143,0.0002141886,0.00008172553,0.00005440248,0.001308832,0.000003217836,0.00009563581],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.003357153,"threshold_uncertainty_score":0.006495833,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1804394028466929,"score_gpt":0.3662605108546846,"score_spread":0.1858211080079918,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}