{"id":"W4207016536","doi":"10.1016/j.autrev.2022.103055","title":"Eculizumab use in catastrophic antiphospholipid syndrome (CAPS): Descriptive analysis from the “CAPS Registry”","year":2022,"lang":"en","type":"review","venue":"Autoimmunity Reviews","topic":"Systemic Lupus Erythematosus Research","field":"Medicine","cited_by":86,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"Department of Obstetrics and Gynecology, University of Wisconsin-Madison; Sorbonne Université; Urmia University of Medical Sciences; Akershus Universitetssykehus; Centre hospitalier universitaire Sainte-Justine; Debreceni Egyetem; McGill University Health Centre; Universidad Nacional Mayor de San Marcos; Gdański Uniwersytet Medyczny; Universidade Federal do Rio de Janeiro; Universidade do Estado do Rio de Janeiro; Shahrekord University of Medical Sciences; Universitetet i Oslo; Mayo Clinic; Tel Aviv University; Tays; Catholic University of Korea; Kagawa University; Fundación Valle del Lili; Cedars-Sinai Medical Center; Department of Haematology, Christian Medical College, Vellore; Universidad de Antioquia; University Hospitals; Central Manchester University Hospitals NHS Foundation Trust","keywords":"Eculizumab; Medicine; Thrombotic microangiopathy; Catastrophic antiphospholipid syndrome; Antiphospholipid syndrome; Atypical hemolytic uremic syndrome; Internal medicine; Pediatrics; Adverse effect; Surgery; Thrombosis; Complement system; Immunology; Antibody; Disease","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","research_integrity","insufficient_payload"],"consensus_categories":["insufficient_payload"],"category_scores_codex":[0.004986533,0.001257676,0.009980584,0.0009829518,0.0004679634,0.0002258866,0.002654246,0.0005650313,0.003231254],"category_scores_gemma":[0.003777749,0.0008029541,0.003520651,0.007371027,0.0004273884,0.0002484654,0.001374406,0.004800026,0.0009710326],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.002443139,"about_ca_system_score_gemma":0.001596974,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01743429,"about_ca_topic_score_gemma":0.0008446352,"domain_scores_codex":[0.9855474,0.007272757,0.003412948,0.001346216,0.001353129,0.001067605],"domain_scores_gemma":[0.9882374,0.002209178,0.001967673,0.00715068,0.0001421311,0.0002929481],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001375672,0.0010213,0.006421629,0.0619516,0.01150945,0.003639297,0.003673529,0.000003236297,0.000003074845,0.00006440924,0.02084595,0.890729],"study_design_scores_gemma":[0.0006665708,0.0001179889,0.0007138634,0.03642746,0.01019279,0.006433305,0.0004968889,0.00001379614,1.224028e-7,0.000006891536,0.9443417,0.0005886792],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.002276874,0.9892679,0.00001607969,0.00007177348,0.0004240499,0.006640035,0.0008162928,0.00009793005,0.0003889984],"genre_scores_gemma":[0.0001721629,0.9891492,0.0002784422,0.0001195859,0.0001059557,0.001778829,0.005603573,0.0001871273,0.00260511],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.9234957,"threshold_uncertainty_score":0.9998068,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1804394028466929,"score_gpt":0.3662605108546846,"score_spread":0.1858211080079918,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}