{"id":"W4210452175","doi":"10.2139/ssrn.4004718","title":"A Promissing Mouse Model for Friedreich Ataxia Progressing Like Human Patients","year":2022,"lang":"en","type":"article","venue":"SSRN Electronic Journal","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Université Laval; Centre hospitalier de l'Université Laval","funders":"","keywords":"Ataxia; Neuroscience; Medicine; Biology; Anatomy; Physical medicine and rehabilitation","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007120835,0.002032604,0.00070617,0.003067407,0.001115535,0.000975127,0.00117537,0.002295033,0.01595143],"category_scores_gemma":[0.0003561363,0.0006070935,0.001272212,0.001130804,0.001138797,0.0008386477,0.0006671037,0.002408279,0.004043187],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005298725,"about_ca_system_score_gemma":0.0006830778,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001253817,"about_ca_topic_score_gemma":0.002405236,"domain_scores_codex":[0.9993389,0.0001191875,0.0001242288,0.0002055077,0.0001372112,0.00007490141],"domain_scores_gemma":[0.9993312,0.0001040861,0.0002355468,0.0001001669,0.00006304788,0.000166037],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.001416486,0.0007602151,0.0008260116,0.0001795357,0.0001367585,0.003687985,0.0002388604,0.0004266778,0.9797039,0.005080918,0.002058353,0.005484206],"study_design_scores_gemma":[0.001905239,0.004097256,0.0118999,0.0003000131,0.001071727,0.02967238,0.0006143278,0.006044967,0.8680137,0.003561067,0.07266244,0.0001570475],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9366667,0.00173166,0.02649519,0.00159478,0.0006977433,0.0007964004,0.0167821,0.002361006,0.0128744],"genre_scores_gemma":[0.9019003,0.002904248,0.02464968,0.0006498045,0.0001591865,0.001022988,0.01101911,0.0006799072,0.05701474],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01595143,"threshold_uncertainty_score":0.05336285,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03062349581363988,"score_gpt":0.2892019087124572,"score_spread":0.2585784128988173,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}