{"id":"W4214535941","doi":"10.22263/2312-4156.2021.6.118","title":"BARTH’S SYNDROME: BRIEF REVIEW AND CLINICAL CASE","year":2021,"lang":"en","type":"article","venue":"Vestnik of Vitebsk State Medical University","topic":"Mitochondrial Function and Pathology","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Institute of Genetics; Directorate for Biological Sciences; National Academy of Sciences of Belarus","keywords":"Medicine; Heart failure; Internal medicine; Cardiology; Digoxin; Differential diagnosis; Disease; Contractility; Heart disease; Pediatrics; Gastroenterology; Endocrinology; Pathology","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003241821,0.00008666187,0.0002566627,0.00002235921,0.00005185273,0.000002918761,0.00008713687,0.0001563671,0.0004637603],"category_scores_gemma":[0.0005960892,0.00008741987,0.00009096383,0.0001097968,0.0002661365,0.000003767152,0.000182831,0.0001537341,0.000008214712],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000005537917,"about_ca_system_score_gemma":0.0002011063,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003181193,"about_ca_topic_score_gemma":0.0001260017,"domain_scores_codex":[0.9989456,0.0002886788,0.0002090799,0.0003037578,0.0001228183,0.0001300435],"domain_scores_gemma":[0.9992592,0.00005087942,0.000071056,0.0002410534,0.0001015052,0.0002763511],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"not_applicable","study_design_scores_codex":[0.001888149,0.003466422,0.09316764,0.005400614,0.002288166,0.3389779,0.0003557019,0.000009714948,0.05322783,0.003491284,0.3238622,0.1738643],"study_design_scores_gemma":[0.003532544,0.001095091,0.006099182,0.0002919884,0.0003394035,0.02564126,0.0001501343,0.00002414674,0.002404248,0.00005128125,0.9600128,0.0003579029],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9890673,0.005123082,0.002344472,0.001504438,0.0003349837,0.0001198224,0.00007383552,0.0000114225,0.001420643],"genre_scores_gemma":[0.7550235,0.2087045,0.00390922,0.01234422,0.0003056292,0.000001316329,0.0004786915,0.00004400638,0.01918884],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6361506,"threshold_uncertainty_score":0.5077851,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01225220287476398,"score_gpt":0.2693506627129882,"score_spread":0.2570984598382243,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}